CHRONIC MULTIFOCAL DEMYELINATING NEUROPATHY SIMULATING MOTOR-NEURON DISEASE

被引:9
作者
DIBELLA, P
LOGULLO, F
DIONISI, L
DANNI, M
SCARPELLI, M
ANGELERI, F
机构
[1] UNIV ANCONA,IST MALATTIE SISTEMA NERVOSO,I-60100 ANCONA,ITALY
[2] UNIV ANCONA,IST ANAT PATOL,I-60100 ANCONA,ITALY
来源
ITALIAN JOURNAL OF NEUROLOGICAL SCIENCES | 1991年 / 12卷 / 01期
关键词
DEMYELINATING NEUROPATHY; MOTOR NEURON DISEASE; CONDUCTION BLOCK;
D O I
10.1007/BF02337624
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We describe a patient with a chronic acquired predominantly motor polyneuropathy. His clinical picture initially led to a diagnosis of lower motor neuron form of amyotrophic lateral sclerosis. However electrophysiological examination revealed multifocal, prevalently proximal, conduction blocks at sites not prone to compression. Distinguishing this unusual polyneuropathy from motor neuron diseases in critical, since the former is a potentially, treatable disorder.
引用
收藏
页码:113 / 118
页数:6
相关论文
共 16 条
[1]   NEUROPATHY WITH ONION BULB FORMATIONS AND PURE MOTOR MANIFESTATIONS [J].
AUER, RN ;
BELL, RB ;
LEE, MA .
CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES, 1989, 16 (02) :194-197
[2]   CONDUCTION BLOCK AND DENERVATION IN GUILLAIN-BARRE POLYNEUROPATHY [J].
BROWN, WF ;
FEASBY, TE .
BRAIN, 1984, 107 (MAR) :219-239
[3]   SLOW RESOLUTION OF MULTIFOCAL WEAKNESS AND FASCICULATION - A REVERSIBLE MOTOR-NEURON SYNDROME [J].
CHAD, DA ;
HAMMER, K ;
SARGENT, J .
NEUROLOGY, 1986, 36 (09) :1260-1263
[4]  
DYCK P J, 1989, Neurology, V39, P391
[5]  
DYCK PJ, 1984, PERIPHERAL NEUROPATH, P2102
[6]   THE PATHOLOGICAL BASIS OF CONDUCTION BLOCK IN HUMAN NEUROPATHIES [J].
FEASBY, TE ;
BROWN, WF ;
GILBERT, JJ ;
HAHN, AF .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1985, 48 (03) :239-244
[7]   MULTIFOCAL DEMYELINATING NEUROPATHY WITH PERSISTENT CONDUCTION BLOCK [J].
LEWIS, RA ;
SUMNER, AJ ;
BROWN, MJ ;
ASBURY, AK .
NEUROLOGY, 1982, 32 (09) :958-964
[8]   IS ISCHEMIA IMPLICATED IN CHRONIC MULTIFOCAL DEMYELINATING NEUROPATHY [J].
NUKADA, H ;
POLLOCK, M ;
HAAS, LF .
NEUROLOGY, 1989, 39 (01) :106-110
[9]   MULTIFOCAL ACQUIRED DEMYELINATING NEUROPATHY MASQUERADING AS MOTOR NEURON DISEASE [J].
PARRY, GJ ;
CLARKE, S .
MUSCLE & NERVE, 1988, 11 (02) :103-107
[10]   GAMMOPATHY WITH PROXIMAL MOTOR AXONOPATHY SIMULATING MOTOR-NEURON DISEASE [J].
PARRY, GJ ;
HOLTZ, SJ ;
BENZEEV, D ;
DRORI, JB .
NEUROLOGY, 1986, 36 (02) :273-276