DIFFUSE LEWY BODY DISEASE PRESENTING WITH SUPRANUCLEAR GAZE PALSY, PARKINSONISM, AND DEMENTIA - A CASE-REPORT

被引:55
作者
DEBRUIN, VMS [1 ]
LEES, AJ [1 ]
DANIEL, SE [1 ]
机构
[1] INST NEUROL,PARKINSONS DIS SOC BRAIN BANK,1 WAKEFIELD ST,LONDON WC1N 1PJ,ENGLAND
关键词
LEWY BODY DISEASE; STEELE-RICHARDSON-OLSZEWSKI SYNDROME;
D O I
10.1002/mds.870070410
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 67-year-old man with a family history of parkinsonism had visual complaints due to difficulty in convergence, which was followed 2 years later by development of bradykinesia and rigidity. The diagnosis of Steele-Richardson-Olszewski syndrome was made on the basis of a supranuclear gaze palsy, bradykinesia, rigidity, and poor response to levodopa. However, subsequent neuropathological examination revealed diffuse Lewy body disease with no evidence of neurofibrillary tangles involving either subcortical or brain stem structures.
引用
收藏
页码:355 / 358
页数:4
相关论文
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