BIOCHEMICAL ABNORMALITY IN - CEREBROTENDINOUS XANTHOMATOSIS - IMPAIRMENT OF BILE-ACID BIOSYNTHESIS ASSOCIATED WITH INCOMPLETE DEGRADATION OF CHOLESTEROL SIDE-CHAIN

被引：190

作者：

SETOGUCHI, T

SALEN, G

TINT, GS

MOSBACH, EH

机构：

[1] CITY NEW YORK INC, PUBL HLTH RES INST, NEW YORK, NY 10016 USA

[2] VET ADM HOSP, NEW YORK, NY 10016 USA

[3] COLL MED & DENT NEW JERSEY, NEWARK, NJ 07103 USA

[4] VET ADM HOSP, E ORANGE, NJ 07019 USA

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1974年 / 53卷 / 05期

关键词：

D O I：

10.1172/JCI107688

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：1393 / 1401

页数：9

共 19 条

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[8] STERO-BILE ACIDS AND BILE STEROLS .47. SYNTHESIS OF 3ALPHA, 7ALPHA, 12ALPHA, 25XI, 26-PENTAHYDROXYCOPROSTANES AND 3ALPHA, 7ALPHA, 12ALPHA, 24XI, 25-PENTAHYDROXYCOPROSTANES [J].

HOSHITA, T .

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[9] HEPATIC SYNTHESIS OF BILE-ACIDS - BIOCHEMICAL STEPS AND MECHANISMS OF RATE CONTROL [J].

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[10]

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