STRUCTURE OF KERATOSULFATE-LIKE MATERIAL IN LIVER FROM A PATIENT WITH GM1-GANGLIOSIDOSIS (BETA-D-GALACTOSIDASE DEFICIENCY)

被引:32
作者
TSAY, GC
DAWSON, G
机构
[1] UNIV CHICAGO,JOSEPH P KENNEDY JR MENTAL RETARDATION RES CTR,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
[2] UNIV CHICAGO,JOSEPH P KENNEDY JR MENTAL RETARDATION RES CTR,PRITZKER SCH MED,DEPT BIOCHEM,CHICAGO,IL 60637
关键词
D O I
10.1016/0006-291X(73)91002-4
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:759 / 766
页数:8
相关论文
共 18 条
[1]  
BHAVANANDAN VP, 1967, J BIOL CHEM, V242, P4352
[2]  
BRAY BA, 1967, J BIOL CHEM, V242, P3373
[3]   ISOLATION AND CHARACTERIZATION OF KERATAN SULFATES FROM LIVER OF A PATIENT WITH GM1-GANGLIOSIDOSIS TYPE-I [J].
CALLAHAN, JW ;
WOLFE, LS .
BIOCHIMICA ET BIOPHYSICA ACTA, 1970, 215 (03) :527-+
[4]   SIMULTANEOUS ESTIMATION OF 6-DEOXY-L-GALACTOSE (L-FUCOSE) D-MANNOSE D-GALACTOSE 2-ACETAMIDO-2-DEOXY-D-GLUCOSE (N-ACETYL-D-GLUCOSAMINE) AND N-ACETYLNEURAMINIC ACID (SIALIC ACID) IN GLYCOPEPTIDES AND GLYCOPROTEINS [J].
CLAMP, JR ;
DAWSON, G ;
HOUGH, L .
BIOCHIMICA ET BIOPHYSICA ACTA, 1967, 148 (02) :342-&
[5]   INVESTIGATIONS ON OLIGOSACCHARIDE UNITS OF AN A MYELOMA GLOBULIN [J].
DAWSON, G ;
CLAMP, JR .
BIOCHEMICAL JOURNAL, 1968, 107 (03) :341-&
[6]  
DAWSON G, 1972, SPHINGOLIPIDS SPHING
[7]   DIE KONSTITUTION DER GANGLIO-N-TETRAOSE UND DES GANGLIOSIDS GI [J].
KUHN, R ;
WIEGANDT, H .
CHEMISCHE BERICHTE-RECUEIL, 1963, 96 (03) :866-&
[8]   3-ACETAMINO-FURAN AUS N-ACETYL-D-GLUCOSAMIN - EIN BEITRAG ZUR THEORIE DER MORGAN-ELSON-REAKTION [J].
KUHN, R ;
KRUGER, G .
CHEMISCHE BERICHTE-RECUEIL, 1956, 89 (06) :1473-1486
[9]   STRUCTURE COMPARISON OF MAJOR MONOSIALOGANGLIOSIDES FROM BRAINS OF NORMAL HUMAN GARGOYLISM AND LATE INFANTILE SYSTEMIC LIPIDOSIS .I. [J].
LEDEEN, R ;
SALSMAN, K ;
GONATAS, J ;
TAGHAVY, A .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1965, 24 (02) :341-&
[10]  
LI YT, 1972, METHODS ENZYMOLOGY, V28