PRENATAL-DIAGNOSIS OF CONGENITAL CYSTIC ADENOMATOID LUNG MALFORMATION - A REPORT OF 7 CASES

被引:16
作者
HEYDANUS, R
STEWART, PA
WLADIMIROFF, JW
LOS, FJ
机构
[1] ACAD HOSP ROTTERDAM, DIJKZIGT, DEPT OBSTET & GYNAECOL, DR MOLEWATERPLEIN 40, 3015 GD ROTTERDAM, NETHERLANDS
[2] ACAD HOSP ROTTERDAM, DIJKZIGT, DIV PRENATAL DIAG, ROTTERDAM, NETHERLANDS
[3] ACAD HOSP ROTTERDAM, DIJKZIGT, DEPT CLIN GENET, ROTTERDAM, NETHERLANDS
关键词
CONGENITAL; CYSTIC; ADENOMATOID; LUNG; MALFORMATION; ULTRASOUND; POLYHYDRAMNIOS; FETAL HYDROPS;
D O I
10.1002/pd.1970130110
中图分类号
Q3 [遗传学];
学科分类号
071007 ; 090102 ;
摘要
Six cases of macrocystic and one case of microcystic congenital adenomatoid lung malformation were diagnosed by ultrasound between 20 and 31 weeks of gestation. Combined polyhydramnios and fetal hydrops was present in three cases, polyhydramnios alone in one case, and isolated fetal hydrops also in one case. In the remaining two cases, both polyhydramnios and fetal hydrops were absent. Fetal outcome was poor, i.e., two terminations of pregnancy, three early neonatal deaths, and two survivors.
引用
收藏
页码:65 / 71
页数:7
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