HYPERKETOTIC STATES DUE TO INHERITED DEFECTS OF KETOLYSIS

被引：40

作者：

SAUDUBRAY, JM

SPECOLA, N

MIDDLETON, B

LOMBES, A

BONNEFONT, JP

JAKOBS, C

VASSAULT, A

CHARPENTIER, C

DAY, R

机构：

[1] HOP NECKER ENFANTS MALAD,DEPT INVEST METAB,F-75743 PARIS 15,FRANCE

[2] FREE UNIV AMSTERDAM,ACAD ZIEKENHUIS,1007 MC AMSTERDAM,NETHERLANDS

[3] UNIV NOTTINGHAM,SCH MED,NOTTINGHAM NG7 2RD,ENGLAND

来源：

ENZYME | 1987年 / 38卷 / 1-4期

关键词：

D O I：

10.1159/000469194

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：80 / 90

页数：11

共 29 条

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[8] VARIANT FORM OF 2-METHYL-3-HYDROXYBUTYRIC AND 2-METHYLACETOACETIC ACIDURIA [J].

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[10]

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