STURGE-WEBER SYNDROME WITHOUT FACIAL NEVUS

被引:33
作者
PASCUALCASTROVIEJO, I
PASCUALPASCUAL, SI
VIANO, J
MARTINEZ, V
COYA, J
机构
[1] SANATORIO NUESTRA SENORA ROSARIO,UNITY IMAGING,MADRID,SPAIN
[2] HOSP LA PAZ,NUCL MED SERV,MADRID,SPAIN
关键词
CT; EPILEPSY; MR; MR ANGIOGRAPHY; MR WITH GD-DTPA; SPECT; STURGE-WEBER SYNDROME;
D O I
10.1055/s-2007-979759
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A patient with Sturge-Weber syndrome without the characteristic facial news presented with focal seizures which were difficult to control and borderline mental level. CT disclosed calcification in the right occipital zone. A marked decrease of the regional cerebral blood flow that extended beyond the abnormalities depicted on CT was seen by SPECT. Venous magnetic resonance (MR) angiography revealed reduction of the superficial cortical veins and prominent deep collateral Venous system in the same side of the cerebral lesion. Cranial MR imaging with Gd-DTPA demonstrated the pial angioma.
引用
收藏
页码:220 / 222
页数:3
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