SYMPTOMATIC HYPERAMMONEMIA CAUSED BY A CONGENITAL PORTOSYSTEMIC SHUNT

被引:43
作者
KITAGAWA, S
GLEASON, WA
NORTHRUP, H
MIDDLEBROOK, MR
UEBERSCHAR, E
机构
[1] UNIV TEXAS, SCH MED, DEPT RADIOL, HOUSTON, TX 77030 USA
[2] HERMANN CHILDRENS HOSP, HOUSTON, TX USA
关键词
D O I
10.1016/S0022-3476(05)80341-5
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A child with trisomy 21 had altered mental status and hyperammonemia at presentation and was found to have a congenital portosystemic shunt as a result of a congenital abnormality of the portal venous system. Anomalies of the portal venous system leading to portosystemic shunting, although they are infrequent, should be considered in the differential diagnosis of hyperammonemia.
引用
收藏
页码:917 / 919
页数:3
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