ENZYMIC DEFECT IN MORQUIOS DISEASE - SPECIFICITY OF N-ACETYLHEXOSAMINE SULFATASES

被引：44

作者：

HORWITZ, AL

DORFMAN, A

机构：

[1] UNIV CHICAGO,PRITZKER SCH MED,JOSEPH P KENNEDY JR MENTAL RETARDAT RES CTR,DEPT BIOCHEM,CHICAGO,IL 60637

[2] UNIV CHICAGO,PRITZKER SCH MED,JOSEPH P KENNEDY JR MENTAL RETARDAT RES CTR,COMM GENET,CHICAGO,IL 60637

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1978年 / 80卷 / 04期

关键词：

D O I：

10.1016/0006-291X(78)91318-9

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：819 / 825

页数：7

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[8] DEFICIENCY OF CHONDROITIN SULFATE N-ACETYLGALACTOSAMINE 4-SULFATE SULFATASE IN MAROTEAUX-LAMY SYNDROME [J].

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