NEUROSARCOIDOSIS - SIGNS, COURSE AND TREATMENT IN 35 CONFIRMED CASES

被引:285
作者
CHAPELON, C
ZIZA, JM
PIETTE, JC
LEVY, Y
RAGUIN, G
WECHSLER, B
BITKER, MO
BLETRY, O
LAPLANE, D
BOUSSER, MG
GODEAU, P
机构
[1] HOP PITIE,SERV UROL,F-75651 PARIS 13,FRANCE
[2] HOP LA PITIE SALPETRIERE,MALAD SYST NERVEUX CLIN,F-75651 PARIS 13,FRANCE
[3] HOP ST ANTOINE,SERV NEUROL,F-75571 PARIS 12,FRANCE
关键词
D O I
10.1097/00005792-199009000-00001
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Sarcoidosis is a multisystem granulomatous disease of unknown etiology and pathogenesis, most commonly affecting young adults. It may present with bilateral hilar lymphadenopathy, pulmonary infiltrates, and skin or eye lesions. Neurologic manifestations are rare, with an estimated frequency of 5% to 6% (22, 32, 80, 97, 99), and have been the subject of only 2 large series (80, 99). Our study of 35 patients with neurosarcoidosis has allowed us to observe a wide variety of clinical manifestations and to evaluate prognosis and treatment in this disorder. © 1990 by Williams & Wilkins.
引用
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页码:261 / 276
页数:16
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