DYSTROPHIN-GLYCOPROTEIN COMPLEX - MOLECULAR-ORGANIZATION AND CRITICAL ROLES IN SKELETAL-MUSCLE

被引:67
作者
SUNADA, Y
CAMPBELL, KP
机构
[1] Howard Hughes Medical Institute, Department Physiology and Biophysics, University Iowa College of Medicine, Iowa City, IA 53243
关键词
D O I
10.1097/00019052-199510000-00010
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Recent molecular and biochemical studies have disclosed the detailed molecular organization of the dystrophin-glycoprotein complex, which links the cytoskeleton to the extracellular matrix. Defects in several components of this complex cause different types of muscular dystrophy. This glycoprotein complex is also involved in clustering and anchoring acetylcholine receptors at the postsynaptic membrane.
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页码:379 / 384
页数:6
相关论文
共 40 条
  • [1] 2 FORMS OF MOUSE SYNTROPHIN, A 58-KD DYSTROPHIN-ASSOCIATED PROTEIN, DIFFER IN PRIMARY STRUCTURE AND TISSUE DISTRIBUTION
    ADAMS, ME
    BUTLER, MH
    DWYER, TM
    PETERS, MF
    MURNANE, AA
    FROEHNER, SC
    [J]. NEURON, 1993, 11 (03) : 531 - 540
  • [2] CLONING OF HUMAN BASIC A1, A DISTINCT 59-KDA DYSTROPHIN-ASSOCIATED PROTEIN ENCODED ON CHROMOSOME 8Q23-24
    AHN, AH
    YOSHIDA, M
    ANDERSON, MS
    FEENER, CA
    SELIG, S
    HAGIWARA, Y
    OZAWA, E
    KUNKEL, LM
    [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1994, 91 (10) : 4446 - 4450
  • [3] SYNTROPHIN BINDS TO AN ALTERNATIVELY SPLICED EXON OF DYSTROPHIN
    AHN, AH
    KUNKEL, LM
    [J]. JOURNAL OF CELL BIOLOGY, 1995, 128 (03) : 363 - 371
  • [4] LAMININ IN ANIMAL-MODELS FOR MUSCULAR-DYSTROPHY - DEFECT OF LAMININ-M IN SKELETAL AND CARDIAC MUSCLES AND PERIPHERAL-NERVE OF THE HOMOZYGOUS DYSTROPHIC DY/DY MICE
    ARAHATA, K
    HAYASHI, YK
    KOGA, R
    GOTO, K
    LEE, JH
    MIYAGOE, Y
    ISHII, H
    TSUKAHARA, T
    TAKEDA, S
    WOO, M
    NONAKA, I
    MATSUZAKI, T
    SUGITA, H
    [J]. PROCEEDINGS OF THE JAPAN ACADEMY SERIES B-PHYSICAL AND BIOLOGICAL SCIENCES, 1993, 69 (10): : 259 - 264
  • [5] BELIN AM, 1995, J BIOL CHEM, V270, P6328
  • [6] IDENTIFICATION AND PURIFICATION OF AN AGRIN RECEPTOR FROM TORPEDO POSTSYNAPTIC MEMBRANES - A HETEROMERIC COMPLEX RELATED TO THE DYSTROGLYCANS
    BOWE, MA
    DEYST, KA
    LESZYK, JD
    FALLON, JR
    [J]. NEURON, 1994, 12 (05) : 1173 - 1180
  • [7] BUTLER MH, 1992, J BIOL CHEM, V267, P6213
  • [8] ROLE FOR DYSTROPHIN-ASSOCIATED GLYCOPROTEINS AND UTROPHIN IN AGRIN-INDUCED ACHR CLUSTERING
    CAMPANELLI, JT
    ROBERDS, SL
    CAMPBELL, KP
    SCHELLER, RH
    [J]. CELL, 1994, 77 (05) : 663 - 674
  • [9] ASSOCIATION OF DYSTROPHIN AND AN INTEGRAL MEMBRANE GLYCOPROTEIN
    CAMPBELL, KP
    KAHL, SD
    [J]. NATURE, 1989, 338 (6212) : 259 - 262
  • [10] ERVASTI JM, 1991, J BIOL CHEM, V266, P9161