DEFICIENCY OF PROTEIN 4.2 IN ERYTHROCYTES FROM A PATIENT WITH A COOMBS NEGATIVE HEMOLYTIC-ANEMIA - EVIDENCE FOR A ROLE OF PROTEIN 4.2 IN STABILIZING ANKYRIN ON THE MEMBRANE

被引:100
作者
RYBICKI, AC
HEATH, R
WOLF, JL
LUBIN, B
SCHWARTZ, RS
机构
[1] CHILDRENS HOSP OAKLAND RES INST,OAKLAND,CA 94609
[2] ALTA BATES HOSP,DEPT MED ONCOL HEMATOL & BONE MARROW TRANSPLANTAT,BERKELEY,CA 94705
关键词
D O I
10.1172/JCI113400
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:893 / 901
页数:9
相关论文
共 29 条
[1]   PARTIAL DEFICIENCY OF ERYTHROCYTE SPECTRIN IN HEREDITARY SPHEROCYTOSIS [J].
AGRE, P ;
CASELLA, JF ;
ZINKHAM, WH ;
MCMILLAN, C ;
BENNETT, V .
NATURE, 1985, 314 (6009) :380-383
[2]  
BARTLETT GR, 1959, J BIOL CHEM, V234, P466
[3]  
BENNETT V, 1980, J BIOL CHEM, V255, P6424
[4]   MEMBRANE ATTACHMENT PROTEIN FOR SPECTRIN IS ASSOCIATED WITH BAND-3 IN HUMAN-ERYTHROCYTE MEMBRANES [J].
BENNETT, V ;
STENBUCK, PJ .
NATURE, 1979, 280 (5722) :468-473
[5]  
BENNETT V, 1977, J BIOL CHEM, V252, P2753
[6]   LABELING OF PROTEINS TO HIGH SPECIFIC RADIOACTIVITIES BY CONJUGATION TO A I-125-CONTAINING ACYLATING AGENT - APPLICATION TO RADIOIMMUNOASSAY [J].
BOLTON, AE ;
HUNTER, WM .
BIOCHEMICAL JOURNAL, 1973, 133 (03) :529-538
[7]  
Dacie J. V., 1975, PRACTICAL HAEMATOLOG, P202
[8]   PREPARATION AND CHEMICAL CHARACTERISTICS OF HEMOGLOBIN-FREE GHOSTS OF HUMAN ERYTHROCYTES [J].
DODGE, JT ;
HANAHAN, DJ ;
MITCHELL, C .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1963, 100 (01) :119-&
[9]   ELECTROPHORETIC ANALYSIS OF MAJOR POLYPEPTIDES OF HUMAN ERYTHROCYTE MEMBRANE [J].
FAIRBANKS, G ;
STECK, TL ;
WALLACH, DFH .
BIOCHEMISTRY, 1971, 10 (13) :2606-+
[10]   THE SPECTRIN MEMBRANE SKELETON OF NORMAL AND ABNORMAL HUMAN-ERYTHROCYTES - A REVIEW [J].
GOODMAN, SR ;
SHIFFER, K .
AMERICAN JOURNAL OF PHYSIOLOGY, 1983, 244 (03) :C121-C141