RENAL HANDLING OF CARNITINE IN CHILDREN WITH CARNITINE DEFICIENCY AND HYPERAMMONEMIA ASSOCIATED WITH VALPROATE THERAPY

被引:68
作者
MATSUDA, I [1 ]
OHTANI, Y [1 ]
NINOMIYA, N [1 ]
机构
[1] KUMAMOTO UNIV, SCH MED, DEPT CHILD DEV, KUMAMOTO 860, JAPAN
关键词
D O I
10.1016/S0022-3476(86)80592-3
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:131 / 134
页数:4
相关论文
共 25 条
[1]  
ADACHI TORU, 1963, J VITAMINOL, V9, P217
[2]   DECREASED SERUM CARNITINE IN VALPROATE INDUCED REYE SYNDROME [J].
BOHLES, H ;
RICHTER, K ;
WAGNERTHIESSEN, E ;
SCHAFER, H .
EUROPEAN JOURNAL OF PEDIATRICS, 1982, 139 (03) :185-186
[3]   CARNITINE [J].
BORUM, PR .
ANNUAL REVIEW OF NUTRITION, 1983, 3 :233-259
[4]   SYSTEMIC CARNITINE DEFICIENCY - A TREATABLE INHERITED LIPID-STORAGE DISEASE PRESENTING AS REYES-SYNDROME [J].
CHAPOY, PR ;
ANGELINI, C ;
BROWN, WJ ;
STIFF, JE ;
SHUG, AL ;
CEDERBAUM, SD .
NEW ENGLAND JOURNAL OF MEDICINE, 1980, 303 (24) :1389-1394
[5]   HYPERAMMONEMIA WITH VALPROIC ACID THERAPY [J].
COULTER, DL ;
ALLEN, RJ .
JOURNAL OF PEDIATRICS, 1981, 99 (02) :317-319
[6]  
COULTER DL, 1984, LANCET, V1, P689
[7]   PRIMARY SYSTEMIC CARNITINE DEFICIENCY .2. RENAL HANDLING OF CARNITINE [J].
ENGEL, AG ;
REBOUCHE, CJ ;
WILSON, DM ;
GLASGOW, AM ;
ROMSHE, CA ;
CRUSE, RP .
NEUROLOGY, 1981, 31 (07) :819-825
[8]  
HASS R, 1981, NEUROLOGY, V31, P1473
[9]  
HATTORI S, 1985, J JPN PEDIATR SOC, V89, P733
[10]   SYNDROME OF SYSTEMIC CARNITINE DEFICIENCY - CLINICAL, MORPHOLOGIC, BIOCHEMICAL, AND PATHOPHYSIOLOGIC FEATURES [J].
KARPATI, G ;
CARPENTER, S ;
ENGEL, AG ;
WATTERS, G ;
ALLEN, J ;
ROTHMAN, S ;
KLASSEN, G ;
MAMER, OA .
NEUROLOGY, 1975, 25 (01) :16-24