ACTIVATOR OF CEREBROSIDE SULFATASE - PURIFICATION FROM HUMAN LIVER AND IDENTIFICATION AS A PROTEIN

被引:117
作者
FISCHER, G [1 ]
JATZKEWITZ, H [1 ]
机构
[1] MAX PLANCK INST PSYCHIAT,NEUROCHEM ABT,KRAEPELIN STR 2,D-8 MUNICH,FED REP GER
来源
HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE | 1975年 / 356卷 / 05期
关键词
D O I
10.1515/bchm2.1975.356.1.605
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:605 / 613
页数:9
相关论文
共 25 条
[1]   ESTIMATION OF MOLECULAR WEIGHTS OF PROTEINS BY SEPHADEX GEL-FILTRATION [J].
ANDREWS, P .
BIOCHEMICAL JOURNAL, 1964, 91 (02) :222-+
[2]   A CONTROLLED STUDY OF ENZYMIC ACTIVITIES IN 3 HUMAN DISORDERS OF GLYCOLIPID METABOLISM [J].
AUSTIN, JH ;
BALASUBRAMANIAN, AS ;
BACHHAWAT, BK ;
BASU, DK ;
SARASWATHI, S ;
PATTABIRAMAN, TN .
JOURNAL OF NEUROCHEMISTRY, 1963, 10 (11) :805-&
[3]   THE ASSAY OF ARYLSULPHATASE-A AND ARYLSULPHATASE-B IN HUMAN URINE [J].
BAUM, H ;
DODGSON, KS ;
SPENCER, B .
CLINICA CHIMICA ACTA, 1959, 4 (03) :453-455
[4]  
FELGENHAUER K, 1970, Clinica Chimica Acta, V27, P305, DOI 10.1016/0009-8981(70)90349-9
[5]   PATTERNS OF ARYLSULFATASES-A AND ARYLSULFATASES-B IN HUMAN NORMAL AND METACHROMATIC LEUCODYSTROPHY TISSUES AND THEIR RELATIONSHIP TO CEREBROSIDE SULFATASE ACTIVITY [J].
HARZER, K ;
STINSHOFF, K ;
MRAZ, W ;
JATZKEWITZ, H .
JOURNAL OF NEUROCHEMISTRY, 1973, 20 (02) :279-287
[6]  
HIRS CHW, 1952, J BIOL CHEM, V195, P669
[7]   GLUCOCEREBROSIDASE - RECONSTITUTION OF ACTIVITY FROM MACROMOLECULAR COMPONENTS [J].
HO, MW ;
OBRIEN, JS ;
RADIN, NS ;
ERICKSON, JS .
BIOCHEMICAL JOURNAL, 1973, 131 (01) :173-176
[8]   GAUCHERS DISEASE - DEFICIENCY OF ACID BETA-GLUCOSIDASE AND RECONSTITUTION OF ENZYME ACTIVITY IN-VITRO [J].
HO, MW ;
OBRIEN, JS .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1971, 68 (11) :2810-&
[9]   ACTIVATOR OF CEREBROSIDE SULFATASE IN HUMAN NORMAL LIVER AND IN CASES OF CONGENITAL METACHROMATIC LEUKODYSTROPHY [J].
JATZKEWI.H ;
STINSHOF.K .
FEBS LETTERS, 1973, 32 (01) :129-131
[10]   CEREBROSIDE-SULPHATASE AND ARYLSULPHATASE A DEFICIENCY IN METACHROMATIC LEUKODYSTROPHY (ML) [J].
JATZKEWITZ, H ;
MEHL, E .
JOURNAL OF NEUROCHEMISTRY, 1969, 16 (01) :19-+