CONGENITAL HYPOPITUITARISM IN FEMALE INFANTS - ITS ASSOCIATION WITH HYPOGLYCEMIA AND HYPO-THYROIDISM

被引:27
作者
KAUSCHANSKY, A
GENEL, M
SMITH, GJW
机构
[1] YALE UNIV,SCH MED,DEPT PEDIAT,PEDIAT ENDOCRINOL SECT,NEW HAVEN,CT 06510
[2] YALE UNIV,SCH MED,DEPT PATHOL,NEW HAVEN,CT 06510
[3] YALE NEW HAVEN HOSP,NEW HAVEN,CT 06504
来源
AMERICAN JOURNAL OF DISEASES OF CHILDREN | 1979年 / 133卷 / 02期
关键词
D O I
10.1001/archpedi.1979.02130020057011
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Congenital hypopituitarism was found in two female infants who had profound hypoglycemia and hypothyroidism. In both infants, death occurred despite recognition of the disorder and institution of appropriate therapy. Autopsy findings showed an absent pituitary gland and sella turcica, with hypoplastic adrenal and thyroid glands, and ovaries in one case, and pituitary gland aplasia with absent thyroid and right adrenal glands plus a hypoplastic left adrenal gland in the other case. © 1979, American Medical Association. All rights reserved.
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页码:165 / 169
页数:5
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