2 UNUSUAL TUMORS OF THE GASTROINTESTINAL-TRACT IN A PATIENT WITH TUBEROUS SCLEROSIS

被引:6
作者
BYARD, RW
PHILLIPS, GE
DARDICK, I
ROBERTSON, E
CARTER, RF
BOURNE, AJ
机构
[1] ADELAIDE CHILDRENS HOSP INC,DEPT CHEM PATHOL,ADELAIDE,SA 5006,AUSTRALIA
[2] INST VET & MED SCI,DEPT TISSUE PATHOL,ADELAIDE,SA,AUSTRALIA
[3] TORONTO GEN HOSP,DEPT PATHOL,TORONTO M5G 1L7,ONTARIO,CANADA
[4] UNIV TORONTO,DEPT PATHOL,TORONTO M5S 1A1,ONTARIO,CANADA
关键词
ADENOMA; COLON; LEIOMYOMA; SALIVARY GLAND; TUBEROUS SCLEROSIS;
D O I
10.1111/j.1440-1754.1991.tb00365.x
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A 16 year old girl with an established diagnosis of tuberous sclerosis presented with a 1 year history of swelling of the left cheek. A 2 cm diameter tumour was excised which showed histological features of a solid variant of a minor salivary gland basal cell adenoma. One year later during laparotomy and excision of multiple renal angiomyolipomas, a 5 cm diameter subserosal tumour was found at the hepatic flexure of the colon. Examination of biopsy material revealed a leiomyoma. This case is presented to demonstrate two tumours that have not to the authors' knowledge been previously described in a young patient with tuberous sclerosis. Although the association may be coincidental, these tumours could represent two rare associations of tuberous sclerosis.
引用
收藏
页码:116 / 119
页数:4
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