REFRACTORY INFANTILE DIARRHEA DUE TO PRIMARY BILE-ACID MALABSORPTION

被引:38
作者
HEUBI, JE
BALISTRERI, WF
PARTIN, JC
SCHUBERT, WK
MCGRAW, CA
机构
[1] UNIV CINCINNATI, CHILDRENS HOSP RES FDN, DEPT PEDIAT, CINCINNATI, OH 45229 USA
[2] UNIV PENN, DEPT PEDIAT, PHILADELPHIA, PA 19104 USA
[3] CHILDRENS HOSP, PHILADELPHIA, PA 19104 USA
关键词
D O I
10.1016/S0022-3476(79)80008-6
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A boy is described who had severe, refractory diarrhea beginning soon after birth. Prolonged parenteralalimentation was required to support life. Investigations of bile acid metabolism showed impaired intestinal absorption of bile acids. Contracted bile acid pool sizes resulted, with low intraluminal bile acid concentrations and severe malabsorption of water and fat. Bile acid malabsorption is a cause of refractory infantile diarrhea. © 1979 The C. V. Mosby Company.
引用
收藏
页码:546 / 551
页数:6
相关论文
共 36 条
[1]   QUANTITATIVE ESTIMATION OF BILE SALTS IN SERUM [J].
ALI, SS ;
JAVITT, NB .
CANADIAN JOURNAL OF BIOCHEMISTRY, 1970, 48 (09) :1054-&
[2]  
AMMON HV, 1973, GASTROENTEROLOGY, V65, P744
[3]   INHIBITION OF ILEAL WATER ABSORPTION BY INTRALUMINAL FATTY-ACIDS - INFLUENCE OF CHAIN-LENGTH, HYDROXYLATION, AND CONJUGATION OF FATTY-ACIDS [J].
AMMON, HV ;
PHILLIPS, SF .
JOURNAL OF CLINICAL INVESTIGATION, 1974, 53 (01) :205-210
[4]  
AMMON HV, 1975, CLIN RES, V23, pA480
[5]  
AUSTAD WI, 1967, GASTROENTEROLOGY, V52, P638
[6]  
BALISTRERI WF, 1978, GASTROENTEROLOGY, V74, P1115
[7]  
BALISTRERI WF, 1978, PEDIATR RES, V12, P429, DOI 10.1203/00006450-197804001-00399
[8]  
BALISTRERI WF, 1977, J PEDIATR, V89, P21
[9]  
DEBARROS SG, 1978, GASTROENTEROLOGY, V74, P1145
[10]  
HEATON KW, 1977, CLIN GASTROENTEROL, V6, P69