DENTATORUBRO-PALLIDOLUYSIAN ATROPHY OF THE MYOCLONUS EPILEPSY TYPE WITH POSTERIOR COLUMN DEGENERATION

被引：15

作者：

PFEIFFER, RF

MCCOMB, RD

机构：

[1] Section of Neurology, University of Nebraska Medical Center, Omaha, Nebraska

[2] Department of Pathology, University of Nebraska Medical Center, Omaha, Nebraska

来源：

MOVEMENT DISORDERS | 1990年 / 5卷 / 02期

关键词：

Dentatorubro pallidoluysian atrophy; Neurodegenerative disease; Ramsay Hunt syndrome;

D O I：

10.1002/mds.870050207

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Dentatorubro‐pallidoluysian atrophy (DRPLA) has a variable clinical presentation but the pathology is routinely confined to cerebellifugal and pallidofugal systems. We present a case of DRPLA of the myoclonus epilepsy type in which prominent posterior column degeneration was added to the pathological picture. This case illustrates the concept that the neurodegenerative diseases can be a continuum of both clinical and pathological presentations. Copyright © 1990 Movement Disorder Society

引用

页码：134 / 138

页数：5

共 20 条

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