UPTAKE AND UTILIZATION OF EXOGENOUS CYSTINE BY CYSTINOTIC AND NORMAL FIBROBLASTS

被引:49
作者
STATES, B
HARRIS, D
SEGAL, S
机构
[1] CHILDRENS HOSP,DIV BIOCHEM DEV & MOLEC DIS,PHILADELPHIA,PA 19146
[2] UNIV PENN,SCH MED,DEPT PEDIAT,PHILADELPHIA,PA 19146
[3] UNIV PENN,SCH MED,DEPT MED,PHILADELPHIA,PA 19146
关键词
D O I
10.1172/JCI107637
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1003 / 1016
页数:14
相关论文
共 30 条
[1]   INTRACELLULAR RATIO OF CYSTEINE AND CYSTINE IN VARIOUS TISSUES [J].
CRAWHALL, JC ;
SEGAL, S .
BIOCHEMICAL JOURNAL, 1967, 105 (02) :891-&
[2]  
FOGH J, 1964, P SOC EXP BIOL MED, V117, P899, DOI 10.3181/00379727-117-29731
[3]  
FOSTER DO, 1969, J BIOL CHEM, V244, P2675
[4]   TRANSPORT OF DIBASIC AMINO-ACIDS, CYSTINE, AND TRYPTOPHAN BY CULTURED HUMAN FIBROBLASTS - ABSENCE OF A DEFECT IN CYSTINURIA AND HARTNUP DISEASE [J].
GROTH, U ;
ROSENBER.LE .
JOURNAL OF CLINICAL INVESTIGATION, 1972, 51 (08) :2130-&
[5]   SERIAL CULTIVATION OF HUMAN DIPLOID CELL STRAINS [J].
HAYFLICK, L ;
MOORHEAD, PS .
EXPERIMENTAL CELL RESEARCH, 1961, 25 (03) :585-+
[6]   HUMAN CYSTINOSIS - INTRACELLULAR DEPOSITION OF CYSTINE [J].
HUMMELER, K ;
ZAJAC, BA ;
GENEL, M ;
HOLTZAPPLE, PG ;
SEGAL, S .
SCIENCE, 1970, 168 (3933) :859-+
[7]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[8]  
MAHONEY M J, 1970, Biochimica et Biophysica Acta, V219, P500, DOI 10.1016/0005-2736(70)90232-4
[10]   ENZYMOLOGY OF AMINO-ACID TRANSPORT [J].
MEISTER, A .
SCIENCE, 1973, 180 (4081) :33-39