ACRALLY OCCURRING DERMATOFIBROSARCOMA PROTUBERANS IN CHILDREN AND ADULTS

被引:38
作者
RABINOWITZ, LG
LUCHETTI, ME
SEGURA, AD
ESTERLY, NB
机构
[1] MED COLL WISCONSIN,DEPT PEDIAT,MILWAUKEE,WI 53226
[2] MED COLL WISCONSIN,DEPT PATHOL,MILWAUKEE,WI 53226
来源
JOURNAL OF DERMATOLOGIC SURGERY AND ONCOLOGY | 1994年 / 20卷 / 10期
关键词
D O I
10.1111/j.1524-4725.1994.tb00447.x
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
BACKGROUND. Dermatofibrosarcoma protuberans (DFSP) arising on the hands and feet is unusual and, at any site, is extremely rare in children. OBJECTIVE. We report a 5-year-old girl who developed DFSP on her hand at 9 months of age. We review the clinical features and treatment of childhood DFSP and of acrally occurring DFSP at all ages. CONCLUSION. DFSP in children develops most often on the back (22.2 %) and at acral sites (14.8 %). It occurs on the hands and feet of children more commonly than in adults. This may be related to the increased frequency of trauma at these sites in children. Mohs micrographic surgery is the treatment of choice for DFSP.
引用
收藏
页码:655 / 659
页数:5
相关论文
共 33 条
[1]  
ANNESSI G, 1933, PEDIATR DERMATOL, V10, P40
[2]  
BASHARA M E, 1992, Journal of Foot Surgery, V31, P160
[3]   DERMATOFIBROSARCOMA PROTUBERANS - A CLINICOPATHOLOGICAL STUDY OF 19 CASES AND REVIEW OF WORLD LITERATURE [J].
BENDIXHANSEN, K ;
MYHREJENSEN, O ;
KAAE, S .
SCANDINAVIAN JOURNAL OF PLASTIC AND RECONSTRUCTIVE SURGERY AND HAND SURGERY, 1983, 17 (03) :247-252
[4]   A REVIEW OF 2,720 LESIONS OF THE FOOT [J].
BERLIN, SJ .
JOURNAL OF THE AMERICAN PODIATRY ASSOCIATION, 1980, 70 (07) :318-324
[5]  
BONNABEAU RC, 1974, ONCOLOGY-BASEL, V29, P1
[6]  
BRENNER W, 1975, CANCER, V36, P1897, DOI 10.1002/1097-0142(197511)36:5<1897::AID-CNCR2820360547>3.0.CO
[7]  
2-X
[8]   DERMATOFIBROSARCOMA PROTUBERANS - STUDY OF 56 CASES [J].
BURKHARDT, BR ;
SOULE, EH ;
WINKELMANN, RK ;
IVINS, JC .
AMERICAN JOURNAL OF SURGERY, 1966, 111 (05) :638-+
[9]   AN UNUSUAL CASE OF DERMATOFIBROSARCOMA PROTUBERANS [J].
COLES, M ;
SMITH, M ;
RANKIN, EA .
JOURNAL OF HAND SURGERY-AMERICAN VOLUME, 1989, 14A (01) :135-138
[10]  
Darier J, 1924, ANN DERMATOL SYPHILI, V5, P545