NIEMANN-PICK DISEASE EXPERIMENTAL-MODEL - SPHINGOMYELINASE REDUCTION INDUCED BY AY-9944

被引：68

作者：

SAKURAGAWA, N

SAKURAGAWA, M

KUWABARA, T

PENTCHEV, PG

BARRANGER, JA

BRADY, RO

机构：

[1] NINCDS,DEV & METAB NEUROL BRANCH,BETHESDA,MD 20014

[2] NEI,VIS RES LAB,BETHESDA,MD 20014

来源：

SCIENCE | 1977年 / 196卷 / 4287期

关键词：

D O I：

10.1126/science.66749

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：317 / 319

页数：3

共 14 条

[1] METABOLISM OF SPHINGOMYELIN .2. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN NIEMANN-PICK DISEASE [J].

BRADY, RO ;

KANFER, JN ;

MOCK, MB ;

FREDRICKSON, DS .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1966, 55 (02) :366-+

[2] ALTERED LEVELS OF TISSUE GLYCOPROTEINS, GANGLIOSIDES, GLYCOSAMINOGLYCANS AND LIPIDS IN NIEMANN-PICKS DISEASE [J].

BRUNNGRABER, EG ;

BERRA, B ;

ZAMBOTTI, V .

CLINICA CHIMICA ACTA, 1973, 48 (02) :173-181

[3]

FREDRICKSON DS, 1972, METABOLIC BASIS INHE, P783

[4] SEPARATION AND IDENTIFICATION OF MONOSACCHARIDES FROM BIOLOGICAL MATERIALS BY THIN-LAYER CHROMATOGRAPHY [J].

GAL, AE .

ANALYTICAL BIOCHEMISTRY, 1968, 24 (03) :452-&

[5] PRACTICAL CHROMOGENIC PROCEDURE FOR DETECTION OF HOMOZYGOTES AND HETEROZYGOUS CARRIERS OF NIEMANN-PICK DISEASE [J].

GAL, AE ;

BRADY, RO ;

HIBBERT, SR ;

PENTCHEV, PG .

NEW ENGLAND JOURNAL OF MEDICINE, 1975, 293 (13) :632-636

[6] STUDIES OF WATER SOLUBLE LIPOPROTEINS IN RAT BRAIN [J].

HERSCHKO.N ;

MCKHANN, GM ;

SHOOTER, EM .

JOURNAL OF NEUROCHEMISTRY, 1968, 15 (03) :161-&

[7] CHANGES IN BRAIN HYDROLYTIC ENZYME-ACTIVITIES IN RATS TREATED WITH CHOLESTEROL-BIOSYNTHESIS INHIBITOR, AY9944 [J].

IGARASHI, M ;

SUZUKI, K ;

CHEN, SM ;

SUZUKI, K .

BRAIN RESEARCH, 1975, 90 (01) :97-114

[8] GAUCHER MOUSE [J].

KANFER, JN ;

LEGLER, G ;

SULLIVAN, J ;

RAGHAVAN, SS ;

MUMFORD, RA .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1975, 67 (01) :85-90

[9] METABOLIC HETEROGENEITY OF SPHINGOMYELIN OF RAT CEREBRUM [J].

LASTENNE.A ;

MANDEL, P ;

FREYSZ, L .

JOURNAL OF NEUROCHEMISTRY, 1972, 19 (03) :831-&

[10]

MARINETTI GV, 1962, J LIPID RES, V3, P1

← 1 2 →