AORTIC-ANEURYSM IN A 5-YEAR-OLD BOY WITH TUBEROUS SCLEROSIS

被引:22
作者
DORTLAND, RWHV
BAX, NMA
HUBER, J
机构
[1] UNIV CHILDRENS HOSP WILHELMINA,DEPT PEDIAT SURG,UTRECHT,NETHERLANDS
[2] UNIV UTRECHT HOSP,INST PATHOL,3511 GV UTRECHT,NETHERLANDS
关键词
CONGENITAL ANEURYSM; ABDOMINAL AORTIC ANEURYSM; TUBEROUS SCLEROSIS; INHERITED CONNECTIVE TISSUE DISEASE;
D O I
10.1016/0022-3468(91)91054-3
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
A 5-year-old boy known to have tuberous sclerosis was admitted with an abdominal aortic aneurysm. The aneurysm was resected and replaced by a bifurcation prosthesis. Follow-up, which amounts up to 4 years, has been uneventful. Prompt recognition and surgical treatment are essential in the management of this rare but potentially lethal condition. © 1991.
引用
收藏
页码:1420 / 1422
页数:3
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