MRI REVEALS MULTIPLE REVERSIBLE CEREBRAL-LESIONS IN AN ATTACK OF ACUTE INTERMITTENT PORPHYRIA

被引:62
作者
KING, PH
BRAGDON, AC
机构
[1] DUKE UNIV,MED CTR,DIV NEUROL,DURHAM,NC 27710
[2] VET ADM MED CTR,SYRACUSE,NY 13210
[3] SUNY HLTH SCI CTR,DEPT NEUROL,SYRACUSE,NY
[4] SUNY HLTH SCI CTR,DEPT PHARMACOL,SYRACUSE,NY
关键词
D O I
10.1212/WNL.41.8.1300
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 20-year-old woman had an attack of acute intermittent porphyria (AIP) with seizures and hallucinations. MRI revealed multiple lesions in both hemispheres. Both the cerebral clinical abnormalities and the MRI lesions resolved following treatment. These findings suggest that a vascular mechanism may underlie the pathogenesis of cerebral dysfunction in AIP.
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收藏
页码:1300 / 1302
页数:3
相关论文
共 10 条
[1]   MR IMAGING OF SYSTEMIC LUPUS-ERYTHEMATOSUS INVOLVING THE BRAIN [J].
AISEN, AM ;
GABRIELSEN, TO ;
MCCUNE, WJ .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1985, 144 (05) :1027-1031
[2]   ACUTE PORPHYRIA - CLINICAL AND PATHOLOGIC OBSERVATIONS [J].
BERG, M .
ARCHIVES OF INTERNAL MEDICINE, 1945, 76 (05) :335-340
[3]   CHANGES IN THE NERVOUS SYSTEM IN ACUTE PORPHYRIA [J].
DENNYBROWN, D ;
SCIARRA, D .
BRAIN, 1945, 68 (01) :1-16
[4]   HYPERTENSIVE ENCEPHALOPATHY - MAGNETIC-RESONANCE IMAGING DEMONSTRATION OF REVERSIBLE CORTICAL AND WHITE MATTER LESIONS [J].
HAUSER, RA ;
LACEY, M ;
KNIGHT, MR .
ARCHIVES OF NEUROLOGY, 1988, 45 (10) :1078-1083
[5]   CHANGES IN THE NERVOUS SYSTEM IN ACUTE PORPHYRIA [J].
HIERONS, R .
BRAIN, 1957, 80 (02) :176-&
[6]  
KAPPAS A, 1989, METABOLIC BASIS INHE, P1320
[7]   TRANSIENT FOCAL ABNORMALITIES OF NEUROIMAGING STUDIES DURING FOCAL STATUS EPILEPTICUS [J].
KRAMER, RE ;
LUDERS, H ;
LESSER, RP ;
WEINSTEIN, MR ;
DINNER, DS ;
MORRIS, HH ;
WYLLIE, E .
EPILEPSIA, 1987, 28 (05) :528-532
[8]   BLINDNESS OF CEREBRAL ORIGIN IN ACUTE INTERMITTENT PORPHYRIA - REPORT OF A CASE AND POSTMORTEM EXAMINATION [J].
LAI, CW ;
HUNG, T ;
LIN, WSJ .
ARCHIVES OF NEUROLOGY, 1977, 34 (05) :310-312
[9]   MR BRAIN-SCANNING IN PATIENTS WITH VASCULITIS - DIFFERENTIATION FROM MULTIPLE-SCLEROSIS [J].
MILLER, DH ;
ORMEROD, IEC ;
GIBSON, A ;
DUBOULAY, EPGH ;
RUDGE, P ;
MCDONALD, WI .
NEURORADIOLOGY, 1987, 29 (03) :226-231
[10]   The photodynamic action of hematoporphyrin [J].
Rask, EN ;
Howell, WH .
AMERICAN JOURNAL OF PHYSIOLOGY, 1928, 84 (02) :363-377