DEMENTIA OF ADULT POLYGLUCOSAN BODY DISEASE - EVIDENCE OF CORTICAL AND SUBCORTICAL DYSFUNCTION

被引：22

作者：

RIFAI, Z

KLITZKE, M

TAWIL, R

KAZEE, AM

SHANSKE, S

DIMAURO, S

GRIGGS, RC

机构：

[1] UNIV ROCHESTER,DEPT PSYCHIAT,ROCHESTER,NY 14642

[2] UNIV ROCHESTER,DEPT PATHOL,ROCHESTER,NY 14642

[3] COLUMBIA PRESBYTERIAN MED CTR,MDA H HOUSTON MERRITT CLIN RES CTR MUSCULAR DYSTROPHY,NEW YORK,NY 10032

来源：

ARCHIVES OF NEUROLOGY | 1994年 / 51卷 / 01期

关键词：

D O I：

10.1001/archneur.1994.00540130124021

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Objectives: To characterize the dementia associated with adult polyglucosan body disease (APBD) and to correlate the cognitive deficits with abnormalities found on magnetic resonance imaging (MRI). Methods: Quantitative neuropsychological testing and MRI in one man with APBD and a review of the literature. Results: The dementia of APBD affects cortical and subcortical functions. The cognitive deficits correlate with MRI findings of cortical atrophy and white-matter abnormalities. Conclusion: Neuropsychological testing and MRI are helpful in the evaluation of patients with APBD.

引用

页码：90 / 94

页数：5

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