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SULFAMIDASE ACTIVITY IN LEUKOCYTES, CULTURED SKIN FIBROBLASTS AND AMNIOTIC CELLS - DIAGNOSIS OF THE SANFILIPPO-A-SYNDROME WITH THE USE OF A RADIOLABELED DISACCHARIDE SUBSTRATE
被引:13
作者
:
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
ELLIOTT, H
论文数:
0
引用数:
0
h-index:
0
ELLIOTT, H
机构
:
来源
:
CLINICAL SCIENCE
|
1981年
/ 61卷
/ 06期
关键词
:
D O I
:
10.1042/cs0610729
中图分类号
:
R-3 [医学研究方法];
R3 [基础医学];
学科分类号
:
1001 ;
摘要
:
引用
收藏
页码:729 / 735
页数:7
相关论文
共 9 条
[1]
MULTIPLE DEFICIENCY OF MUCOPOLYSACCHARIDE SULFATASES IN MUCOSULFATIDOSIS
BASNER, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
BASNER, R
FIGURA, KV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
FIGURA, KV
GLOSSL, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
GLOSSL, J
KLEIN, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
KLEIN, U
KRESSE, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
KRESSE, H
MLEKUSCH, W
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
MLEKUSCH, W
[J].
PEDIATRIC RESEARCH,
1979,
13
(12)
: 1316
-
1318
[2]
POSTNATAL AND PRENATAL ASSESSMENT OF ALPHA-L-IDURONIDASE DEFICIENCY WITH A RADIOLABELED NATURAL SUBSTRATE
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
MULLER, V
论文数:
0
引用数:
0
h-index:
0
MULLER, V
POLLARD, AC
论文数:
0
引用数:
0
h-index:
0
POLLARD, AC
[J].
CLINICAL SCIENCE,
1979,
56
(06)
: 591
-
599
[3]
RADIOLABELED OLIGOSACCHARIDES AS SUBSTRATES FOR THE ESTIMATION OF SULFAMIDASE AND THE DETECTION OF THE SANFILIPPO TYPE-A SYNDROME
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
ELLIOTT, H
论文数:
0
引用数:
0
h-index:
0
ELLIOTT, H
[J].
CLINICA CHIMICA ACTA,
1981,
112
(01)
: 55
-
66
[4]
DIAGNOSIS OF GAUCHERS DISEASE AND NIEMANN-PICK DISEASE WITH SMALL SAMPLES OF VENOUS BLOOD
KAMPINE, JP
论文数:
0
引用数:
0
h-index:
0
KAMPINE, JP
BRADY, RO
论文数:
0
引用数:
0
h-index:
0
BRADY, RO
KANFER, JN
论文数:
0
引用数:
0
h-index:
0
KANFER, JN
FELD, M
论文数:
0
引用数:
0
h-index:
0
FELD, M
SHAPIRO, D
论文数:
0
引用数:
0
h-index:
0
SHAPIRO, D
[J].
SCIENCE,
1967,
155
(3758)
: 86
-
&
[5]
MUCOPOLYSACCHARIDOSIS III A (SANFILIPPO A DISEASE) - DEFICIENCY OF A HEPARIN SULFAMIDASE IN SKIN FIBROBLASTS AND LEUKOCYTES
KRESSE, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER,INST PHYSIOL CHEM,MUNSTER,WEST GERMANY
UNIV MUNSTER,INST PHYSIOL CHEM,MUNSTER,WEST GERMANY
KRESSE, H
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1973,
54
(03)
: 1111
-
1118
[6]
KRESSE H, 1972, J BIOL CHEM, V247, P2164
[7]
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[8]
SANFILIPPO A SYNDROME - SULFAMIDASE DEFICIENCY IN CULTURED SKIN FIBROBLASTS AND LIVER
MATALON, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CHICAGO,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
MATALON, R
DORFMAN, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CHICAGO,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
DORFMAN, A
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1974,
54
(04)
: 907
-
912
[9]
LABORATORY DIAGNOSIS OF SANFILIPPO DISEASE
WHITEMAN, P
论文数:
0
引用数:
0
h-index:
0
机构:
INST CHILD HLTH,DEPT CHEM PATHOL,LONDON WC1N 1EH,ENGLAND
INST CHILD HLTH,DEPT CHEM PATHOL,LONDON WC1N 1EH,ENGLAND
WHITEMAN, P
YOUNG, E
论文数:
0
引用数:
0
h-index:
0
机构:
INST CHILD HLTH,DEPT CHEM PATHOL,LONDON WC1N 1EH,ENGLAND
INST CHILD HLTH,DEPT CHEM PATHOL,LONDON WC1N 1EH,ENGLAND
YOUNG, E
[J].
CLINICA CHIMICA ACTA,
1977,
76
(01)
: 139
-
147
←
1
→
共 9 条
[1]
MULTIPLE DEFICIENCY OF MUCOPOLYSACCHARIDE SULFATASES IN MUCOSULFATIDOSIS
BASNER, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
BASNER, R
FIGURA, KV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
FIGURA, KV
GLOSSL, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
GLOSSL, J
KLEIN, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
KLEIN, U
KRESSE, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
KRESSE, H
MLEKUSCH, W
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
UNIV GRAZ,INST MED CHEM,A-8036 GRAZ,AUSTRIA
MLEKUSCH, W
[J].
PEDIATRIC RESEARCH,
1979,
13
(12)
: 1316
-
1318
[2]
POSTNATAL AND PRENATAL ASSESSMENT OF ALPHA-L-IDURONIDASE DEFICIENCY WITH A RADIOLABELED NATURAL SUBSTRATE
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
MULLER, V
论文数:
0
引用数:
0
h-index:
0
MULLER, V
POLLARD, AC
论文数:
0
引用数:
0
h-index:
0
POLLARD, AC
[J].
CLINICAL SCIENCE,
1979,
56
(06)
: 591
-
599
[3]
RADIOLABELED OLIGOSACCHARIDES AS SUBSTRATES FOR THE ESTIMATION OF SULFAMIDASE AND THE DETECTION OF THE SANFILIPPO TYPE-A SYNDROME
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
ELLIOTT, H
论文数:
0
引用数:
0
h-index:
0
ELLIOTT, H
[J].
CLINICA CHIMICA ACTA,
1981,
112
(01)
: 55
-
66
[4]
DIAGNOSIS OF GAUCHERS DISEASE AND NIEMANN-PICK DISEASE WITH SMALL SAMPLES OF VENOUS BLOOD
KAMPINE, JP
论文数:
0
引用数:
0
h-index:
0
KAMPINE, JP
BRADY, RO
论文数:
0
引用数:
0
h-index:
0
BRADY, RO
KANFER, JN
论文数:
0
引用数:
0
h-index:
0
KANFER, JN
FELD, M
论文数:
0
引用数:
0
h-index:
0
FELD, M
SHAPIRO, D
论文数:
0
引用数:
0
h-index:
0
SHAPIRO, D
[J].
SCIENCE,
1967,
155
(3758)
: 86
-
&
[5]
MUCOPOLYSACCHARIDOSIS III A (SANFILIPPO A DISEASE) - DEFICIENCY OF A HEPARIN SULFAMIDASE IN SKIN FIBROBLASTS AND LEUKOCYTES
KRESSE, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER,INST PHYSIOL CHEM,MUNSTER,WEST GERMANY
UNIV MUNSTER,INST PHYSIOL CHEM,MUNSTER,WEST GERMANY
KRESSE, H
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1973,
54
(03)
: 1111
-
1118
[6]
KRESSE H, 1972, J BIOL CHEM, V247, P2164
[7]
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[8]
SANFILIPPO A SYNDROME - SULFAMIDASE DEFICIENCY IN CULTURED SKIN FIBROBLASTS AND LIVER
MATALON, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CHICAGO,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
MATALON, R
DORFMAN, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CHICAGO,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
DORFMAN, A
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1974,
54
(04)
: 907
-
912
[9]
LABORATORY DIAGNOSIS OF SANFILIPPO DISEASE
WHITEMAN, P
论文数:
0
引用数:
0
h-index:
0
机构:
INST CHILD HLTH,DEPT CHEM PATHOL,LONDON WC1N 1EH,ENGLAND
INST CHILD HLTH,DEPT CHEM PATHOL,LONDON WC1N 1EH,ENGLAND
WHITEMAN, P
YOUNG, E
论文数:
0
引用数:
0
h-index:
0
机构:
INST CHILD HLTH,DEPT CHEM PATHOL,LONDON WC1N 1EH,ENGLAND
INST CHILD HLTH,DEPT CHEM PATHOL,LONDON WC1N 1EH,ENGLAND
YOUNG, E
[J].
CLINICA CHIMICA ACTA,
1977,
76
(01)
: 139
-
147
←
1
→