PARTIAL SPLENECTOMY IN GAUCHERS-DISEASE - FOLLOW-UP REPORT

被引:3
作者
BARMAOR, JA
机构
[1] Department of Pediatric Surgery, Rambam Medical Center, The Bruce Rappaport Faculty of Medicine, Haifa
关键词
GAUCHERS DISEASE; PARTIAL SPLENECTOMY;
D O I
10.1016/0022-3468(93)90032-G
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
This is a follow-up report of three children who had partial splenectomy and are suffering from Gaucher's disease. A few years following partial splenectomy in every patient, the remaining spleen enlarged and hypersplenism reappeared; partial splenectomy did not prevent bone destruction if it already existed before partial splenectomy. Treatment with Ceredase parallel with partial splenectomy may have theoretical and practical advantages. © 1993.
引用
收藏
页码:686 / 688
页数:3
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