INHERITED HUMAN PRION DISEASES

被引:158
作者
HSIAO, K [1 ]
PRUSINER, SB [1 ]
机构
[1] UNIV CALIF SAN FRANCISCO, DEPT BIOCHEM & BIOPHYS, SAN FRANCISCO, CA 94143 USA
关键词
D O I
10.1212/WNL.40.12.1820
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:1820 / 1827
页数:8
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[1]   FAMILIAL CEREBRAL AMYLOIDOSIS AND SPONGIFORM ENCEPHALOPATHY [J].
ADAM, J ;
CROW, TJ ;
DUCHEN, LW ;
SCARAVILLI, F ;
SPOKES, E .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1982, 45 (01) :37-45
[2]   EXCEPTIONALLY SMALL SIZE OF SCRAPIE AGENT [J].
ALPER, T ;
HAIG, DA ;
CLARKE, MC .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1966, 22 (03) :278-&
[4]   CEREBELLAR PLAQUES IN FAMILIAL ALZHEIMERS-DISEASE (GERSTMANN-STRAUSSLER-SCHEINKER VARIANT-QUESTIONABLE) [J].
AZZARELLI, B ;
MULLER, J ;
GHETTI, B ;
DYKEN, M ;
CONNEALLY, PM .
ACTA NEUROPATHOLOGICA, 1985, 65 (3-4) :235-246
[5]   RESTRICTION SITES CONTAINING CPG SHOW A HIGHER FREQUENCY OF POLYMORPHISM IN HUMAN DNA [J].
BARKER, D ;
SCHAFER, M ;
WHITE, R .
CELL, 1984, 36 (01) :131-138
[6]   CREUTZFELDT-JAKOB DISEASE PRION PROTEINS IN HUMAN BRAINS [J].
BOCKMAN, JM ;
KINGSBURY, DT ;
MCKINLEY, MP ;
BENDHEIM, PE ;
PRUSINER, SB .
NEW ENGLAND JOURNAL OF MEDICINE, 1985, 312 (02) :73-78
[7]   IMMUNOBLOTTING OF CREUTZFELDT-JAKOB DISEASE PRION PROTEINS - HOST SPECIES-SPECIFIC EPITOPES [J].
BOCKMAN, JM ;
PRUSINER, SB ;
TATEISHI, J ;
KINGSBURY, DT .
ANNALS OF NEUROLOGY, 1987, 21 (06) :589-595
[8]   SCRAPIE AND CELLULAR PRION PROTEINS DIFFER IN THEIR KINETICS OF SYNTHESIS AND TOPOLOGY IN CULTURED-CELLS [J].
BORCHELT, DR ;
SCOTT, M ;
TARABOULOS, A ;
STAHL, N ;
PRUSINER, SB .
JOURNAL OF CELL BIOLOGY, 1990, 110 (03) :743-752
[9]   DIAGNOSIS OF CREUTZFELDT-JAKOB DISEASE BY WESTERN-BLOT IDENTIFICATION OF MARKER PROTEIN IN HUMAN-BRAIN TISSUE [J].
BROWN, P ;
COKERVANN, M ;
POMEROY, K ;
FRANKO, M ;
ASHER, DM ;
GIBBS, CJ ;
GAJDUSEK, DC .
NEW ENGLAND JOURNAL OF MEDICINE, 1986, 314 (09) :547-551
[10]   AMYLOID PLAQUES IN BRAINS OF MICE INFECTED WITH SCRAPIE - MORPHOLOGICAL VARIATION AND STAINING PROPERTIES [J].
BRUCE, ME ;
FRASER, H .
NEUROPATHOLOGY AND APPLIED NEUROBIOLOGY, 1975, 1 (02) :189-202