PEROXISOMAL DISORDERS IN NEUROLOGY

被引:164
作者
WANDERS, RJA
HEYMANS, HSA
SCHUTGENS, RBH
BARTH, PG
VANDENBOSCH, H
TAGER, JM
机构
[1] UNIV HOSP AMSTERDAM,DEPT NEUROL,1105 AZ AMSTERDAM,NETHERLANDS
[2] STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
[3] UNIV AMSTERDAM,BIOCHEM LAB,AMSTERDAM,NETHERLANDS
关键词
D O I
10.1016/0022-510X(88)90203-1
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:1 / 39
页数:39
相关论文
共 228 条
[1]   A POSSIBLE RELATIONSHIP BETWEEN CONCENTRATION OF MICROPEROXISOMES AND MYELINATION [J].
ADAMO, AM ;
ALOISE, PA ;
PASQUINI, JM .
INTERNATIONAL JOURNAL OF DEVELOPMENTAL NEUROSCIENCE, 1986, 4 (06) :513-517
[2]   GLYCOGEN ACCUMULATION IN THE CENTRAL NERVOUS-SYSTEM IN THE CEREBRO-HEPATO-RENAL SYNDROME - REPORT OF A CASE WITH ULTRASTRUCTURAL STUDIES [J].
AGAMANOLIS, DP ;
PATRE, S .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1979, 41 (03) :325-342
[3]   CEREBRO-HEPATO-RENAL SYNDROME - REPORT OF A CASE WITH HISTOCHEMICAL AND ULTRASTRUCTURAL OBSERVATIONS [J].
AGAMANOLIS, DP ;
ROBINSON, HB ;
TIMMONS, GD .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1976, 35 (03) :226-246
[4]  
APPELKVIST EL, 1987, PEROXISOMES BIOL MED, P53
[5]   HYPERPIPECOLIC ACIDEMIA - OCCURRENCE IN AN INFANT WITH CLINICAL FINDINGS OF THE CEREBROHEPATORENAL (ZELLWEGER) SYNDROME [J].
ARNESON, DW ;
TIPTON, RE ;
WARD, JC .
ARCHIVES OF NEUROLOGY, 1982, 39 (11) :713-716
[6]   MICROPEROXISOMES IN CENTRAL NERVOUS-SYSTEM OF POSTNATAL RAT [J].
ARNOLD, G ;
HOLTZMAN, E .
BRAIN RESEARCH, 1978, 155 (01) :1-17
[7]   NEONATAL ADRENOLEUKODYSTROPHY [J].
AUBOURG, P ;
SCOTTO, J ;
ROCCHICCIOLI, F ;
FELDMANNPAUTRAT, D ;
ROBAIN, O .
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1986, 49 (01) :77-86
[8]   THE CEREBRO-HEPATO-RENAL (ZELLWEGER) SYNDROME - LAMELLAR LIPID PROFILES IN ADRENOCORTICAL, HEPATIC MESENCHYMAL, ASTROCYTE CELLS AND INCREASED LEVELS OF VERY LONG-CHAIN FATTY-ACIDS AND PHYTANIC ACID IN THE PLASMA [J].
AUBOURG, P ;
ROBAIN, O ;
ROCCHICCIOLI, F ;
DANCEA, S ;
SCOTTO, J .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1985, 69 (1-2) :9-25
[9]   LINKAGE OF ADRENOLEUKODYSTROPHY TO A POLYMORPHIC DNA PROBE [J].
AUBOURG, PR ;
SACK, GH ;
MEYERS, DA ;
LEASE, JJ ;
MOSER, HW .
ANNALS OF NEUROLOGY, 1987, 21 (04) :349-352
[10]   A MILDER VARIANT OF ZELLWEGER SYNDROME [J].
BARTH, PG ;
SCHUTGENS, RBH ;
BAKKEREN, JAJM ;
DINGEMANS, KP ;
HEYMANS, HSA ;
DOUWES, AC ;
VANDERKLEIVANMOORSEL, JM .
EUROPEAN JOURNAL OF PEDIATRICS, 1985, 144 (04) :338-342