THE ROLE OF THIAMIN IN MAPLE SYRUP URINE DISEASE

被引：22

作者：

ELSAS, LJ ^{[1
]}

DANNER, DJ ^{[1
]}

机构：

[1] EMORY UNIV,SCH MED,DEPT BIOCHEM,ATLANTA,GA 30322

来源：

ANNALS OF THE NEW YORK ACADEMY OF SCIENCES | 1982年 / 378卷 / MAR期

关键词：

D O I：

10.1111/j.1749-6632.1982.tb31214.x

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：404 / 421

页数：18

共 27 条

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[5] STABILIZATION OF MAMMALIAN LIVER BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE BY THIAMIN PYROPHOSPHATE [J].

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LEMMON, SK ;

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[6]

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[7] SUBCELLULAR-DISTRIBUTION AND COFACTOR FUNCTION OF HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE IN NORMAL AND MUTANT CULTURED SKIN FIBROBLASTS [J].

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[8] THIAMINE INCREASES SPECIFIC ACTIVITY OF HUMAN LIVER BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE [J].

DANNER, DJ ;

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[9] INVIVO AND INVITRO RESPONSE OF HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE TO THIAMINE AND THIAMINE PYROPHOSPHATE [J].

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[10]

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