CLINICAL AND IMMUNOHISTOCHEMICAL STUDIES OF SUBEPENDYMAL GIANT-CELL ASTROCYTOMAS ASSOCIATED WITH TUBEROUS SCLEROSIS

被引:13
作者
IWASAKI, Y
YOSHIKAWA, H
SASAKI, M
SUGAI, K
SUZUKI, H
HIRAYAMA, Y
SAKURAGAWA, N
ARIMA, M
TAKASHIMA, S
AOKI, N
机构
[1] NATL CTR NEUROSCI & PSYCHIAT,NATL INST NEUROSCI,DIV MENTAL RETARDAT & BIRTH DEFECT RES,KODAIRA,TOKYO,JAPAN
[2] NATL CTR HOSP MENTAL NERVOUS & MUSCULAR DISORDERS DIV CHILD NEUROL,KODAIRA,TOKYO,JAPAN
[3] TOKYO METROPOLITAN FUCHU GEN HOSP,DEPT NEUROSURG,FUCHU,TOKYO,JAPAN
关键词
brain tumor; cystic lesion; immunohistochemical study; rapid progression; Tuberous sclerosis;
D O I
10.1016/S0387-7604(12)80211-7
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Two cases of TS associated with brain tumors had severe psychomotor retardation and early onset of long-term intractable convulsions, compared with cases without tumors. In one case, the tumor was partially cystic and progressed rapidly. Immunohistochemical studies of neuron specific enolase, glial fibrillary acidic protein and myelin basic protein revealed differences in positivity between cell types and between cases. These results suggested that the origin of the tumor cells could be variably differentiated cells. © 1990, All rights reserved.
引用
收藏
页码:478 / 481
页数:4
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