CEROID STORAGE DISEASE COMPLICATED BY RUPTURE OF SPLEEN

被引:23
作者
WINKLER, HH
FRAME, B
SAEED, SM
SPINDLER, AC
BROUILLETTE, JN
机构
关键词
D O I
10.1016/0002-9343(69)90013-8
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A nineteen year old male Negro with a ruptured, enlarged spleen is described. Histochemical studies demonstrated that the spleen was infiltrated by histiocytes laden with ceroid, an insoluble, acid-fast, sudanophilic, periodic acid-Schiff-positive, autofluorescent pigment. The prolonged ingestion of increased amounts of polyunsaturated fatty acids was considered to be etiologically significant. © 1969.
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页码:297 / +
页数:1
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