MOTOR-NEURON DISEASE AND DEMENTIA REPORTED AMONG 13 MEMBERS OF A SINGLE FAMILY

被引：48

作者：

GUNNARSSON, LG ^{[1
]}

DAHLBOM, K ^{[1
]}

STRANDMAN, E ^{[1
]}

机构：

[1] OREBRO MED CTR HOSP,DEPT NEUROPHYSIOL,S-70185 OREBRO,SWEDEN

来源：

ACTA NEUROLOGICA SCANDINAVICA | 1991年 / 84卷 / 05期

关键词：

AMYTROPHIC LATERAL SCLEROSIS; HEREDITY;

D O I：

10.1111/j.1600-0404.1991.tb04983.x

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

All 49 members of four generations of a family were identified. In the first three generations eight members were afflicted with dementia, whereas in the fourth generation only one was demented but three of four were afflicted with motor neuron disease and they also had slight cognitive deficiencies. The pattern of heredity is compatible with dominant autosomal inheritance. Neuropsychological testing revealed affection mostly of the frontal lobes. A pedigree and six case reports are presented.

引用

页码：429 / 433

页数：5

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