INVESTIGATION OF ALPHA-GALACTOSIDASE DEFICIENCY IN FABRYS-DISEASE USING ANTIBODIES AGAINST PURIFIED ENZYME

被引:35
作者
RIETRA, PJGM
MOLENAAR, JL
HAMERS, MN
TAGER, JM
BORST, P
机构
[1] UNIV AMSTERDAM,JAN SWAMMERDAM INST,LAB BIOCHEM,AFD MED ENZYMOL,EERSTE CONSTANTIJN HUIJGENS STR,AMSTERDAM,NETHERLANDS
[2] NETHERLANDS RED CROSS,BLOOD TRANSF SERV,CENT LAB,PLESMAN LAAN 125,AMSTERDAM,NETHERLANDS
[3] UNIV AMSTERDAM,BCP JANSEN INST,LAB BIOCHEM,PLANTAGE MUIDERGRACHT 12,AMSTERDAM C,NETHERLANDS
来源
EUROPEAN JOURNAL OF BIOCHEMISTRY | 1974年 / 46卷 / 01期
关键词
D O I
10.1111/j.1432-1033.1974.tb03600.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:89 / 98
页数:10
相关论文
共 27 条
[1]  
BEUTLER E, 1972, AM J HUM GENET, V24, P237
[2]  
BEUTLER E, 1972, J BIOL CHEM, V247, P7195
[3]  
BOYER SH, 1973, LANCET, V2, P654
[4]   ENZYMATIC DEFECT IN FABRYS DISEASE - CERAMIDETRIHEXOSIDASE DEFICIENCY [J].
BRADY, RO ;
GAL, AE ;
BRADLEY, RM ;
MARTENSS.E ;
WARSHAW, AL ;
LASTER, L .
NEW ENGLAND JOURNAL OF MEDICINE, 1967, 276 (21) :1163-&
[5]   REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - USE OF PURIFIED CERAMIDETRIHEXOSIDASE IN FABRYS-DISEASE [J].
BRADY, RO ;
TALLMAN, JF ;
JOHNSON, WG ;
GAL, AE ;
LEAHY, WR ;
QUIRK, JM ;
DEKABAN, AS .
NEW ENGLAND JOURNAL OF MEDICINE, 1973, 289 (01) :9-14
[6]   IMMUNOLOGICAL PROPERTIES OF N-ACETYL-BETA-D-GLUCOSAMINIDASE OF NORMAL HUMAN LIVER AND OF GM2-GANGLIOSIDOSIS LIVER [J].
CARROLL, M ;
ROBINSON, D .
BIOCHEMICAL JOURNAL, 1973, 131 (01) :91-&
[7]  
CRAWHALL JC, 1972, SCIENCE, V177, P527, DOI 10.1126/science.177.4048.527
[8]  
CUATRECASAS P, 1971, METHODS ENZYMOL, V22
[9]  
de Barsy T, 1972, Eur J Biochem, V31, P156
[10]  
DEDUVE C, 1964, FED PROC, V23, P1045