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LONG-TERM INTRACELLULAR RETENTION OF HEXOSAMINIDASE-A BY TAY-SACHS DISEASE BRAIN AND LUNG-CELLS INVITRO
被引:4
作者
:
BROOKS, SE
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
BROOKS, SE
[
1
]
HOFFMAN, LM
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
HOFFMAN, LM
[
1
]
AMSTERDAM, D
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
AMSTERDAM, D
[
1
]
ADACHI, M
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
ADACHI, M
[
1
]
SCHNECK, L
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
SCHNECK, L
[
1
]
机构
:
[1]
SUNY DOWNSTATE MED CTR, BROOKLYN, NY 11203 USA
来源
:
JOURNAL OF NEUROSCIENCE RESEARCH
|
1981年
/ 6卷
/ 03期
关键词
:
D O I
:
10.1002/jnr.490060313
中图分类号
:
Q189 [神经科学];
学科分类号
:
071006 ;
摘要
:
引用
收藏
页码:381 / 388
页数:8
相关论文
共 17 条
[1]
AMSTERDAM D, 1975, GANGLIOSIDOSES, P265
[2]
EFFECT OF LECTINS ON ENDOCYTOSIS AND SECRETION OF LYSOSOMAL ENZYMES BY CULTURED FIBROBLASTS
[J].
BEECK, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
BEECK, H
;
ULLRICH, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
ULLRICH, K
;
VONFIGURA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
VONFIGURA, K
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1979,
583
(02)
:179
-188
[3]
ENZYME REPLACEMENT TREATMENT FOR TAY-SACHS DISEASE BRAIN-CELLS IN CULTURE UTILIZING CONCANAVALIN A-MEDIATED HEXOSAMINIDASE-A UPTAKE - BIOCHEMICAL AND MORPHOLOGICAL EVIDENCE OF GM2 MOBILIZATION
[J].
BROOKS, SE
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
BROOKS, SE
;
HOFFMAN, LM
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
HOFFMAN, LM
;
ADACHI, M
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
ADACHI, M
;
AMSTERDAM, D
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
AMSTERDAM, D
;
SCHNECK, L
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SCHNECK, L
.
ACTA NEUROPATHOLOGICA,
1980,
50
(01)
:9
-17
[4]
IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES
[J].
BROT, FE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
BROT, FE
;
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
GLASER, JH
;
ROOZEN, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
ROOZEN, KJ
;
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
SLY, WS
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1974,
57
(01)
:1
-8
[5]
SECRETION OF BETA-HEXOSAMINIDASE BY CULTURED HUMAN-SKIN FIBROBLASTS - KINETICS, EFFECT OF TEMPERATURE, CELL DENSITY, SERUM CONCENTRATION AND PH
[J].
FIGURA, KV
论文数:
0
引用数:
0
h-index:
0
FIGURA, KV
.
EXPERIMENTAL CELL RESEARCH,
1978,
111
(01)
:15
-21
[6]
CONCANAVALIN A MEDIATED UPTAKE OF ENZYMES BY FIBROBLASTS
[J].
GONZALEZNORIEGA, A
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT GENET, ST LOUIS, MO 63130 USA
GONZALEZNORIEGA, A
;
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT GENET, ST LOUIS, MO 63130 USA
SLY, WS
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1978,
85
(01)
:174
-182
[7]
HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES
[J].
HICKMAN, S
论文数:
0
引用数:
0
h-index:
0
HICKMAN, S
;
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
NEUFELD, EF
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1972,
49
(04)
:992
-&
[8]
RECOGNITION MARKER REQUIRED FOR UPTAKE OF A LYSOSOMAL ENZYME BY CULTURED FIBROBLASTS
[J].
HICKMAN, S
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
HICKMAN, S
;
SHAPIRO, LJ
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
SHAPIRO, LJ
;
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
NEUFELD, EF
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1974,
57
(01)
:55
-61
[9]
GM2 GANGLIOSIDE IN FETAL TAY-SACHS DISEASE BRAIN CULTURES - MODEL SYSTEM FOR DISEASE
[J].
HOFFMAN, LM
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,ISAAC ALBERT RES INST,DEPT NEUROL,BROOKLYN,NY 11203
HOFFMAN, LM
;
AMSTERDAM, D
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,ISAAC ALBERT RES INST,DEPT NEUROL,BROOKLYN,NY 11203
AMSTERDAM, D
;
SCHNECK, L
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,ISAAC ALBERT RES INST,DEPT NEUROL,BROOKLYN,NY 11203
SCHNECK, L
.
BRAIN RESEARCH,
1976,
111
(01)
:109
-117
[10]
GLYCOSPHINGOLIPIDS IN FETAL TAY-SACHS DISEASE BRAIN AND LUNG CULTURES
[J].
HOFFMAN, LM
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,CTR NEUROSCI,BROOKLYN,NY 11203
HOFFMAN, LM
;
AMSTERDAM, D
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,CTR NEUROSCI,BROOKLYN,NY 11203
AMSTERDAM, D
;
BROOKS, SE
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,CTR NEUROSCI,BROOKLYN,NY 11203
BROOKS, SE
;
SCHNECK, L
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,CTR NEUROSCI,BROOKLYN,NY 11203
SCHNECK, L
.
JOURNAL OF NEUROCHEMISTRY,
1977,
29
(03)
:551
-559
←
1
2
→
共 17 条
[1]
AMSTERDAM D, 1975, GANGLIOSIDOSES, P265
[2]
EFFECT OF LECTINS ON ENDOCYTOSIS AND SECRETION OF LYSOSOMAL ENZYMES BY CULTURED FIBROBLASTS
[J].
BEECK, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
BEECK, H
;
ULLRICH, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
ULLRICH, K
;
VONFIGURA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
UNIV MUNSTER, INST PHYS CHEM, D-4400 MUNSTER, FED REP GER
VONFIGURA, K
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1979,
583
(02)
:179
-188
[3]
ENZYME REPLACEMENT TREATMENT FOR TAY-SACHS DISEASE BRAIN-CELLS IN CULTURE UTILIZING CONCANAVALIN A-MEDIATED HEXOSAMINIDASE-A UPTAKE - BIOCHEMICAL AND MORPHOLOGICAL EVIDENCE OF GM2 MOBILIZATION
[J].
BROOKS, SE
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
BROOKS, SE
;
HOFFMAN, LM
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
HOFFMAN, LM
;
ADACHI, M
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
ADACHI, M
;
AMSTERDAM, D
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
AMSTERDAM, D
;
SCHNECK, L
论文数:
0
引用数:
0
h-index:
0
机构:
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SUNY DOWNSTATE MED CTR,BROOKLYN,NY 11203
SCHNECK, L
.
ACTA NEUROPATHOLOGICA,
1980,
50
(01)
:9
-17
[4]
IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES
[J].
BROT, FE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
BROT, FE
;
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
GLASER, JH
;
ROOZEN, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
ROOZEN, KJ
;
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
SLY, WS
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1974,
57
(01)
:1
-8
[5]
SECRETION OF BETA-HEXOSAMINIDASE BY CULTURED HUMAN-SKIN FIBROBLASTS - KINETICS, EFFECT OF TEMPERATURE, CELL DENSITY, SERUM CONCENTRATION AND PH
[J].
FIGURA, KV
论文数:
0
引用数:
0
h-index:
0
FIGURA, KV
.
EXPERIMENTAL CELL RESEARCH,
1978,
111
(01)
:15
-21
[6]
CONCANAVALIN A MEDIATED UPTAKE OF ENZYMES BY FIBROBLASTS
[J].
GONZALEZNORIEGA, A
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT GENET, ST LOUIS, MO 63130 USA
GONZALEZNORIEGA, A
;
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT GENET, ST LOUIS, MO 63130 USA
SLY, WS
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1978,
85
(01)
:174
-182
[7]
HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES
[J].
HICKMAN, S
论文数:
0
引用数:
0
h-index:
0
HICKMAN, S
;
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
NEUFELD, EF
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1972,
49
(04)
:992
-&
[8]
RECOGNITION MARKER REQUIRED FOR UPTAKE OF A LYSOSOMAL ENZYME BY CULTURED FIBROBLASTS
[J].
HICKMAN, S
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
HICKMAN, S
;
SHAPIRO, LJ
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
SHAPIRO, LJ
;
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
机构:
NIAMDD,BETHESDA,MD 20014
NIAMDD,BETHESDA,MD 20014
NEUFELD, EF
.
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1974,
57
(01)
:55
-61
[9]
GM2 GANGLIOSIDE IN FETAL TAY-SACHS DISEASE BRAIN CULTURES - MODEL SYSTEM FOR DISEASE
[J].
HOFFMAN, LM
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,ISAAC ALBERT RES INST,DEPT NEUROL,BROOKLYN,NY 11203
HOFFMAN, LM
;
AMSTERDAM, D
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,ISAAC ALBERT RES INST,DEPT NEUROL,BROOKLYN,NY 11203
AMSTERDAM, D
;
SCHNECK, L
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,ISAAC ALBERT RES INST,DEPT NEUROL,BROOKLYN,NY 11203
SCHNECK, L
.
BRAIN RESEARCH,
1976,
111
(01)
:109
-117
[10]
GLYCOSPHINGOLIPIDS IN FETAL TAY-SACHS DISEASE BRAIN AND LUNG CULTURES
[J].
HOFFMAN, LM
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,CTR NEUROSCI,BROOKLYN,NY 11203
HOFFMAN, LM
;
AMSTERDAM, D
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,CTR NEUROSCI,BROOKLYN,NY 11203
AMSTERDAM, D
;
BROOKS, SE
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,CTR NEUROSCI,BROOKLYN,NY 11203
BROOKS, SE
;
SCHNECK, L
论文数:
0
引用数:
0
h-index:
0
机构:
KINGSBROOK JEWISH MED CTR,CTR NEUROSCI,BROOKLYN,NY 11203
SCHNECK, L
.
JOURNAL OF NEUROCHEMISTRY,
1977,
29
(03)
:551
-559
←
1
2
→