共 47 条
[5]
PURIFICATION AND CHARACTERIZATION OF AN ACTIVATOR PROTEIN FOR THE DEGRADATION OF GLYCOLIPID-GM2 AND GLYCOLIPID-GA2 BY HEXOSAMINIDASE-A
[J].
HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE,
1979, 360 (12)
:1837-1849
[6]
COMPLEXING OF GLYCOLIPIDS AND THEIR TRANSFER BETWEEN MEMBRANES BY THE ACTIVATOR PROTEIN FOR DEGRADATION OF LYSOSOMAL GANGLIOSIDE GM2
[J].
EUROPEAN JOURNAL OF BIOCHEMISTRY,
1982, 123 (02)
:455-464
[7]
DUBOIS G, 1975, NEW ENGL J MED, V293, P302
[9]
DUBOIS G, 1977, AM J HUM GENET, V29, P191
[10]
DULANEY JT, 1977, PRACTICAL ENZYMOLOGY, P137