COMPLEXING OF GLYCOLIPIDS AND THEIR TRANSFER BETWEEN MEMBRANES BY THE ACTIVATOR PROTEIN FOR DEGRADATION OF LYSOSOMAL GANGLIOSIDE GM2

被引:144
作者
CONZELMANN, E
BURG, J
STEPHAN, G
SANDHOFF, K
机构
来源
EUROPEAN JOURNAL OF BIOCHEMISTRY | 1982年 / 123卷 / 02期
关键词
D O I
10.1111/j.1432-1033.1982.tb19789.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:455 / 464
页数:10
相关论文
共 36 条
[1]   HYDROLYSIS OF DISIALO AND TRISIALO GANGLIOSIDES IN MICELLAR AND LIPOSOMAL DISPERSION BY BACTERIAL NEURAMINIDASES [J].
CESTARO, B ;
BARENHOLZ, Y ;
GATT, S .
BIOCHEMISTRY, 1980, 19 (04) :615-619
[3]   PURIFICATION AND CHARACTERIZATION OF AN ACTIVATOR PROTEIN FOR THE DEGRADATION OF GLYCOLIPID-GM2 AND GLYCOLIPID-GA2 BY HEXOSAMINIDASE-A [J].
CONZELMANN, E ;
SANDHOFF, K .
HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE, 1979, 360 (12) :1837-1849
[4]  
CONZELMANN E, 1979, THESIS U MUNCHEN
[5]  
DEKRUIJFF B, 1976, BIOCH BIOPHYS ACTA, V443, P629
[6]   ACTIVATOR OF CEREBROSIDE SULFATASE - BINDING STUDIES WITH ENZYME AND SUBSTRATE DEMONSTRATING DETERGENT FUNCTION OF ACTIVATOR PROTEIN [J].
FISCHER, G ;
JATZKEWITZ, H .
BIOCHIMICA ET BIOPHYSICA ACTA, 1977, 481 (02) :561-572
[7]   ACTIVATOR OF CEREBROSIDE-SULFATASE - MODEL OF ACTIVATION [J].
FISCHER, G ;
JATZKEWITZ, H .
BIOCHIMICA ET BIOPHYSICA ACTA, 1978, 528 (01) :69-76
[8]   ENZYMES OF COMPLEX LIPID-METABOLISM [J].
GATT, S ;
BARENHOLZ, Y .
ANNUAL REVIEW OF BIOCHEMISTRY, 1973, 42 :61-90
[9]  
HECHTMAN P, 1980, AM J HUM GENET, V32, pA42
[10]   TRANSFER OF PHOSPHATIDYLCHOLINE BETWEEN LIPOSOMES [J].
HELLINGS, JA ;
KAMP, HH ;
WIRTZ, KWA ;
VANDEENE.LL .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1974, 47 (03) :601-605