AB-VARIANT OF INFANTILE GM2 GANGLIOSIDOSIS - DEFICIENCY OF A FACTOR NECESSARY FOR STIMULATION OF HEXOSAMINIDASE A-CATALYZED DEGRADATION OF GANGLIOSIDE GM2 AND GLYCOLIPID GA2

被引：261

作者：

CONZELMANN, E

SANDHOFF, K

机构：

来源：

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA | 1978年 / 75卷 / 08期

关键词：

D O I：

10.1073/pnas.75.8.3979

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：3979 / 3983

页数：5

共 16 条

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[6] CHARACTERIZATION OF AN ACTIVATING FACTOR REQUIRED FOR HYDROLYSIS OF GM2 GANGLIOSIDE CATALYZED BY HEXOSAMINIDASE-A [J].

HECHTMAN, P .

CANADIAN JOURNAL OF BIOCHEMISTRY, 1977, 55 (04) :315-324

[7] GAUCHERS DISEASE - DEFICIENCY OF ACID BETA-GLUCOSIDASE AND RECONSTITUTION OF ENZYME ACTIVITY IN-VITRO [J].

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