METABOLIC DISORDER SIMILAR TO ZELLWEGER SYNDROME WITH HEPATIC ACATALASIA AND ABSENCE OF PEROXISOMES, ALTERED CONTENT AND REDOX STATE OF CYTOCHROMES, AND INFANTILE CIRRHOSIS WITH HEMOSIDEROSIS

被引:63
作者
VERSMOLD, HT
BREMER, HI
HERZOG, V
SIEGEL, G
BASSEWITZ, DBV
IRLE, U
VOSS, HV
LOMBECK, I
BRAUSER, B
机构
[1] UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
[2] UNIV MUNICH,DEPT CELL BIOL,D-8000 MUNICH 2,FED REP GER
[3] PROF HESS CHILDRENS HOSP,D-2800 BREMEN,BUNDES REPUBLIK
[4] UNIV MUNICH,INST PHYSIOL CHEM & PHYS BIOCHEM,D-8000 MUNICH 2,FED REP GER
[5] UNIV DUSSELDORF,CHILDRENS HOSP 3,D-4000 DUSSELDORF 1,BUNDES REPUBLIK
[6] FREE UNIV BERLIN,INST PHYSIOL,D-1000 BERLIN 33,FED REP GER
[7] UNIV MUNSTER,INST PATHOL,D-4400 MUNSTER,FED REP GER
关键词
D O I
10.1007/BF00441934
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:261 / 275
页数:15
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