METABOLIC DISORDER SIMILAR TO ZELLWEGER SYNDROME WITH HEPATIC ACATALASIA AND ABSENCE OF PEROXISOMES, ALTERED CONTENT AND REDOX STATE OF CYTOCHROMES, AND INFANTILE CIRRHOSIS WITH HEMOSIDEROSIS

被引：63

作者：

VERSMOLD, HT

BREMER, HI

HERZOG, V

SIEGEL, G

BASSEWITZ, DBV

IRLE, U

VOSS, HV

LOMBECK, I

BRAUSER, B

机构：

[1] UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER

[2] UNIV MUNICH,DEPT CELL BIOL,D-8000 MUNICH 2,FED REP GER

[3] PROF HESS CHILDRENS HOSP,D-2800 BREMEN,BUNDES REPUBLIK

[4] UNIV MUNICH,INST PHYSIOL CHEM & PHYS BIOCHEM,D-8000 MUNICH 2,FED REP GER

[5] UNIV DUSSELDORF,CHILDRENS HOSP 3,D-4000 DUSSELDORF 1,BUNDES REPUBLIK

[6] FREE UNIV BERLIN,INST PHYSIOL,D-1000 BERLIN 33,FED REP GER

[7] UNIV MUNSTER,INST PATHOL,D-4400 MUNSTER,FED REP GER

来源：

EUROPEAN JOURNAL OF PEDIATRICS | 1977年 / 124卷 / 04期

关键词：

D O I：

10.1007/BF00441934

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：261 / 275

页数：15

共 50 条

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