DEFICIENCY OF THE PYRUVATE-DEHYDROGENASE COMPONENT IN PYRUVATE-DEHYDROGENASE COMPLEX DEFICIENT HUMAN-FIBROBLASTS - IMMUNOLOGICAL IDENTIFICATION

被引：54

作者：

HO, L

HU, CWC

PACKMAN, S

PATEL, MS

机构：

[1] CASE WESTERN RESERVE UNIV,SCH MED,DEPT BIOCHEM,CLEVELAND,OH 44106

[2] UNIV CALIF SAN FRANCISCO,SCH MED,DEPT PEDIAT,SAN FRANCISCO,CA 94143

来源：

关键词：

D O I：

10.1172/JCI112651

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：844 / 847

页数：4

共 19 条

[1] DISORDERS OF PYRUVATE METABOLISM
BLASS, JP
[J]. NEUROLOGY, 1979, 29 (03) : 280 - 286
[2] CAUTRECASAS P, 1976, ADV PROTEIN CHEM, V30, P251
[3] INDUCTION OF THE BRANCHED-CHAIN 2-OXO ACID DEHYDROGENASE COMPLEX IN 3T3-L1 ADIPOCYTES DURING DIFFERENTIATION
CHUANG, DT
HU, CWC
PATEL, MS
[J]. BIOCHEMICAL JOURNAL, 1983, 214 (01) : 177 - 181
[4] COMPONENT-X - AN IMMUNOLOGICALLY DISTINCT POLYPEPTIDE ASSOCIATED WITH MAMMALIAN PYRUVATE-DEHYDROGENASE MULTI-ENZYME COMPLEX
DEMARCUCCI, O
LINDSAY, JG
[J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 149 (03): : 641 - 648
[5] Hurn B A, 1980, Methods Enzymol, V70, P104
[6] JOHNSTON K, 1984, PEDIATRICS, V74, P1034
[7] KRETZSCHMAR HA, 1986, PEDIATRICS
[8] LOWRY OH, 1951, J BIOL CHEM, V193, P265
[9] MILD PROCEDURE FOR THE RAPID RELEASE OF CYTOPLASMIC ENZYMES FROM CULTURED ANIMAL-CELLS
MACKALL, J
MEREDITH, M
LANE, MD
[J]. ANALYTICAL BIOCHEMISTRY, 1979, 95 (01) : 270 - 274
[10] MATUDA S, 1984, CLIN CHIM ACTA, V140, P59