SURGICAL-TREATMENT OF INTRACTABLE SEIZURES DUE TO HYPOTHALAMIC HAMARTOMA

被引:73
作者
NISHIO, S [1 ]
MORIOKA, T [1 ]
FUKUI, M [1 ]
GOTO, Y [1 ]
机构
[1] KYUSHU UNIV,FAC MED,NEUROL INST,DEPT NEUROSURG,FUKUOKA 812,JAPAN
关键词
HYPOTHALAMIC NEOPLASMS; NEUROLOGIC MANIFESTATIONS; NEUROSURGERY; SEIZURES; ELECTROENCEPHALOGRAPHY;
D O I
10.1111/j.1528-1157.1994.tb02470.x
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 6.5-year-old boy developed seizures at age 2.8 years consisting of episodes of unconsciousness and laughing attacks. By age 6 years, multiple seizure types, including generalized tonic-clonic (GTC), complex partial (CPS) and akinetic seizures, and drop attacks were occurring several times daily. EEG showed multifocal epileptic discharges. Antiepileptic drugs (AEDs) did not control the seizures. With progression of the epilepsy, cognitive deterioration developed. There were no manifestations of precocious puberty. Neuroimaging disclosed a suprasellar mass in continuity with the hypothalamus, and a diagnosis of hypothalamic hamartoma was made. After surgical resection of the hamartoma, the seizures were completely alleviated, and the epileptic EEG discharges disappeared. Improvement of mental function was also noted.
引用
收藏
页码:514 / 519
页数:6
相关论文
共 23 条
[1]   NEUROSURGICAL TREATMENT OF HYPOTHALAMIC HAMARTOMAS CAUSING PRECOCIOUS PUBERTY [J].
ALBRIGHT, AL ;
LEE, PA .
JOURNAL OF NEUROSURGERY, 1993, 78 (01) :77-82
[2]   NEUROPEPTIDES - A ROLE AS ENDOGENOUS MEDIATORS OR MODULATORS OF EPILEPTIC PHENOMENA [J].
BAJOREK, JG ;
LEE, RJ ;
LOMAX, P .
ANNALS OF NEUROLOGY, 1984, 16 :S31-S38
[3]  
BALAGURA S, 1979, SURG NEUROL, V11, P315
[4]   HYPOTHALAMIC HAMARTOMAS AND ICTAL LAUGHTER - EVOLUTION OF A CHARACTERISTIC EPILEPTIC SYNDROME AND DIAGNOSTIC-VALUE OF MAGNETIC-RESONANCE IMAGING [J].
BERKOVIC, SF ;
ANDERMANN, F ;
MELANSON, D ;
ETHIER, RE ;
FEINDEL, W ;
GLOOR, P .
ANNALS OF NEUROLOGY, 1988, 23 (05) :429-439
[5]  
BERKOVIC SF, 1979, NEUROLOGY, V37, P993
[6]   GELASTIC SEIZURES, PRECOCIOUS PUBERTY, AND HYPOTHALAMIC HAMARTOMA [J].
BRENINGSTALL, GN .
NEUROLOGY, 1985, 35 (08) :1180-1183
[7]   CURSIVE EPILEPSY AND GELASTIC EPILEPSY [J].
CHEN, RC ;
FORSTER, FM .
NEUROLOGY, 1973, 23 (10) :1019-1029
[8]  
CSCINO GD, 1991, EPILEPSIA S3, V32, P97
[9]  
CURATOLO P, 1984, DEV MED CHILD NEUROL, V26, P509
[10]   HAMARTOMAS OF THE TUBER CINEREUM [J].
DIEBLER, C ;
PONSOT, G .
NEURORADIOLOGY, 1983, 25 (02) :93-101