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ALTERATIONS IN NEURON MORPHOLOGY IN MUCOPOLYSACCHARIDOSIS TYPE-I - A GOLGI-STUDY
被引:35
作者
:
WALKLEY, SU
论文数:
0
引用数:
0
h-index:
0
WALKLEY, SU
HASKINS, ME
论文数:
0
引用数:
0
h-index:
0
HASKINS, ME
SHULL, RM
论文数:
0
引用数:
0
h-index:
0
SHULL, RM
机构
:
来源
:
ACTA NEUROPATHOLOGICA
|
1988年
/ 75卷
/ 06期
关键词
:
D O I
:
10.1007/BF00686207
中图分类号
:
R74 [神经病学与精神病学];
学科分类号
:
摘要
:
引用
收藏
页码:611 / 620
页数:10
相关论文
共 30 条
[1]
DECREASED GANGLIOSIDE NEURAMINIDASE ACTIVITY IN FIBROBLASTS FROM MUCOPOLYSACCHARIDOSIS PATIENTS - INHIBITION OF THE ACTIVITY INVITRO BY SULFATED GLYCOSAMINOGLYCANS AND OTHER COMPOUNDS
BAUMKOTTER, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER
UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER
BAUMKOTTER, J
CANTZ, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER
UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER
CANTZ, M
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1983,
761
(02)
: 163
-
170
[2]
NEUROCHEMICAL CHARACTERIZATION OF CANINE ALPHA-L-IDURONIDASE DEFICIENCY DISEASE (MODEL OF HUMAN MUCOPOLYSACCHARIDOSIS-I)
CONSTANTOPOULOS, G
论文数:
0
引用数:
0
h-index:
0
机构:
NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
CONSTANTOPOULOS, G
SHULL, RM
论文数:
0
引用数:
0
h-index:
0
机构:
NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
SHULL, RM
HASTINGS, N
论文数:
0
引用数:
0
h-index:
0
机构:
NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
HASTINGS, N
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
机构:
NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
NEUFELD, EF
[J].
JOURNAL OF NEUROCHEMISTRY,
1985,
45
(04)
: 1213
-
1217
[3]
NEUROCHEMISTRY OF MUCOPOLYSACCHARIDOSES - BRAIN LIPIDS AND LYSOSOMAL ENZYMES IN PATIENTS WITH 4 TYPES OF MUCOPOLYSACCHARIDOSIS AND IN NORMAL CONTROLS
CONSTANTOPOULOS, G
论文数:
0
引用数:
0
h-index:
0
CONSTANTOPOULOS, G
DEKABAN, AS
论文数:
0
引用数:
0
h-index:
0
DEKABAN, AS
[J].
JOURNAL OF NEUROCHEMISTRY,
1978,
30
(05)
: 965
-
973
[4]
MUCOPOLYSACCHARIDOSIS TYPE-IH, TYPE-IS, TYPE-II, AND TYPE-IIIA - GLYCOSAMINOGLYCANS AND LIPIDS OF ISOLATED BRAIN-CELLS AND OTHER FRACTIONS FROM AUTOPSIED TISSUES
CONSTANTOPOULOS, G
论文数:
0
引用数:
0
h-index:
0
机构:
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
CONSTANTOPOULOS, G
IQBAL, K
论文数:
0
引用数:
0
h-index:
0
机构:
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
IQBAL, K
DEKABAN, AS
论文数:
0
引用数:
0
h-index:
0
机构:
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
DEKABAN, AS
[J].
JOURNAL OF NEUROCHEMISTRY,
1980,
34
(06)
: 1399
-
1411
[5]
GM2 GANGLIOSIDOSIS IN A JAPANESE SPANIEL
CUMMINGS, JF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
CUMMINGS, JF
WOOD, PA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
WOOD, PA
WALKLEY, SU
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
WALKLEY, SU
DELAHUNTA, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
DELAHUNTA, A
DEFOREST, ME
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
DEFOREST, ME
[J].
ACTA NEUROPATHOLOGICA,
1985,
67
(3-4)
: 247
-
253
[6]
ALPHA-L-IDURONIDASE DEFICIENCY IN A CAT - MODEL OF MUCOPOLYSACCHARIDOSIS-I
HASKINS, ME
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
HASKINS, ME
JEZYK, PF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
JEZYK, PF
DESNICK, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
DESNICK, RJ
MCDONOUGH, SK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
MCDONOUGH, SK
PATTERSON, DF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
PATTERSON, DF
[J].
PEDIATRIC RESEARCH,
1979,
13
(11)
: 1294
-
1297
[7]
HASKINS ME, 1983, AM J PATHOL, V112, P27
[8]
ANTAGONISTIC ACTION OF CHONDROITIN SULFATE AND CETYLPYRIDINIUM CHLORIDE ON HUMAN LIVER BETA-GALACTOSIDASE
KINT, JA
论文数:
0
引用数:
0
h-index:
0
机构:
AKAD ZIEKENHUIS,KLIN KINDERZIEKTEN,GHENT,BELGIUM
AKAD ZIEKENHUIS,KLIN KINDERZIEKTEN,GHENT,BELGIUM
KINT, JA
[J].
FEBS LETTERS,
1973,
36
(01)
: 53
-
56
[9]
BIOLOGY OF GANGLIOSIDES - NEURITOGENIC AND NEURONOTROPHIC PROPERTIES
LEDEEN, RW
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT BIOCHEM,BRONX,NY 10461
YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT BIOCHEM,BRONX,NY 10461
LEDEEN, RW
[J].
JOURNAL OF NEUROSCIENCE RESEARCH,
1984,
12
(2-3)
: 147
-
159
[10]
MCKUSICK VA, 1983, METABOLIC BASIS INHE, P751
←
1
2
3
→
共 30 条
[1]
DECREASED GANGLIOSIDE NEURAMINIDASE ACTIVITY IN FIBROBLASTS FROM MUCOPOLYSACCHARIDOSIS PATIENTS - INHIBITION OF THE ACTIVITY INVITRO BY SULFATED GLYCOSAMINOGLYCANS AND OTHER COMPOUNDS
BAUMKOTTER, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER
UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER
BAUMKOTTER, J
CANTZ, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER
UNIV HEIDELBERG,DEPT PATHOCHEM & GEN NEUROCHEM,D-6900 HEIDELBERG,FED REP GER
CANTZ, M
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1983,
761
(02)
: 163
-
170
[2]
NEUROCHEMICAL CHARACTERIZATION OF CANINE ALPHA-L-IDURONIDASE DEFICIENCY DISEASE (MODEL OF HUMAN MUCOPOLYSACCHARIDOSIS-I)
CONSTANTOPOULOS, G
论文数:
0
引用数:
0
h-index:
0
机构:
NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
CONSTANTOPOULOS, G
SHULL, RM
论文数:
0
引用数:
0
h-index:
0
机构:
NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
SHULL, RM
HASTINGS, N
论文数:
0
引用数:
0
h-index:
0
机构:
NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
HASTINGS, N
NEUFELD, EF
论文数:
0
引用数:
0
h-index:
0
机构:
NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
NEUFELD, EF
[J].
JOURNAL OF NEUROCHEMISTRY,
1985,
45
(04)
: 1213
-
1217
[3]
NEUROCHEMISTRY OF MUCOPOLYSACCHARIDOSES - BRAIN LIPIDS AND LYSOSOMAL ENZYMES IN PATIENTS WITH 4 TYPES OF MUCOPOLYSACCHARIDOSIS AND IN NORMAL CONTROLS
CONSTANTOPOULOS, G
论文数:
0
引用数:
0
h-index:
0
CONSTANTOPOULOS, G
DEKABAN, AS
论文数:
0
引用数:
0
h-index:
0
DEKABAN, AS
[J].
JOURNAL OF NEUROCHEMISTRY,
1978,
30
(05)
: 965
-
973
[4]
MUCOPOLYSACCHARIDOSIS TYPE-IH, TYPE-IS, TYPE-II, AND TYPE-IIIA - GLYCOSAMINOGLYCANS AND LIPIDS OF ISOLATED BRAIN-CELLS AND OTHER FRACTIONS FROM AUTOPSIED TISSUES
CONSTANTOPOULOS, G
论文数:
0
引用数:
0
h-index:
0
机构:
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
CONSTANTOPOULOS, G
IQBAL, K
论文数:
0
引用数:
0
h-index:
0
机构:
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
IQBAL, K
DEKABAN, AS
论文数:
0
引用数:
0
h-index:
0
机构:
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
NEW YORK STATE INST BASIC RES MENTAL RETARDAT,STATEN ISL,NY 10314
DEKABAN, AS
[J].
JOURNAL OF NEUROCHEMISTRY,
1980,
34
(06)
: 1399
-
1411
[5]
GM2 GANGLIOSIDOSIS IN A JAPANESE SPANIEL
CUMMINGS, JF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
CUMMINGS, JF
WOOD, PA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
WOOD, PA
WALKLEY, SU
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
WALKLEY, SU
DELAHUNTA, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
DELAHUNTA, A
DEFOREST, ME
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV ALABAMA,DEPT COMPARAT MED,BIRMINGHAM,AL 35294
DEFOREST, ME
[J].
ACTA NEUROPATHOLOGICA,
1985,
67
(3-4)
: 247
-
253
[6]
ALPHA-L-IDURONIDASE DEFICIENCY IN A CAT - MODEL OF MUCOPOLYSACCHARIDOSIS-I
HASKINS, ME
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
HASKINS, ME
JEZYK, PF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
JEZYK, PF
DESNICK, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
DESNICK, RJ
MCDONOUGH, SK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
MCDONOUGH, SK
PATTERSON, DF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PENN,SCH VET MED,MED GENET SECT,PHILADELPHIA,PA 19174
PATTERSON, DF
[J].
PEDIATRIC RESEARCH,
1979,
13
(11)
: 1294
-
1297
[7]
HASKINS ME, 1983, AM J PATHOL, V112, P27
[8]
ANTAGONISTIC ACTION OF CHONDROITIN SULFATE AND CETYLPYRIDINIUM CHLORIDE ON HUMAN LIVER BETA-GALACTOSIDASE
KINT, JA
论文数:
0
引用数:
0
h-index:
0
机构:
AKAD ZIEKENHUIS,KLIN KINDERZIEKTEN,GHENT,BELGIUM
AKAD ZIEKENHUIS,KLIN KINDERZIEKTEN,GHENT,BELGIUM
KINT, JA
[J].
FEBS LETTERS,
1973,
36
(01)
: 53
-
56
[9]
BIOLOGY OF GANGLIOSIDES - NEURITOGENIC AND NEURONOTROPHIC PROPERTIES
LEDEEN, RW
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT BIOCHEM,BRONX,NY 10461
YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT BIOCHEM,BRONX,NY 10461
LEDEEN, RW
[J].
JOURNAL OF NEUROSCIENCE RESEARCH,
1984,
12
(2-3)
: 147
-
159
[10]
MCKUSICK VA, 1983, METABOLIC BASIS INHE, P751
←
1
2
3
→