THE NOSOLOGY OF CREUTZFELDT-JAKOB-DISEASE AND CONDITIONS RELATED TO THE ACCUMULATION OF PRPCJD IN THE NERVOUS-SYSTEM

被引：66

作者：

RICHARDSON, EP

MASTERS, CL

机构：

[1] UNIV MELBOURNE,DEPT PATHOL,PARKVILLE,VIC 3052,AUSTRALIA

[2] MASSACHUSETTS GEN HOSP,CHARLES S KUBIK LAB NEUROPATHOL,BOSTON,MA 02114

来源：

BRAIN PATHOLOGY | 1995年 / 5卷 / 01期

关键词：

D O I：

10.1111/j.1750-3639.1995.tb00575.x

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Although typical cases of Creutzfeldt-Jakob disease are readily recognized pathologically and clinically, variant forms often pose a diagnostic challenge. From the 1920's, when this disease was first characterized, until quite recently diagnosis relied heavily on morphologic changes. New advances in immunoassays and PrP gene analysis now provide important adjuncts in recognizing the spectrum of disorders of PrP metabolism associated with these transmissible encephalopathies.

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页码：33 / 41

页数：9

相关论文

共 99 条

[1] DIFFERENT SUSCEPTIBILITIES OF THE GENICULATE AND EXTRAGENICULATE VISUAL PATHWAYS TO HUMAN CREUTZFELDT-JAKOB DISEASE (A COMBINED NEUROPHYSIOLOGICAL-NEUROPATHOLOGICAL STUDY) [J].

AGUGLIA, U ;

GAMBARELLI, D ;

FARNARIER, G ;

QUATTRONE, A .

ELECTROENCEPHALOGRAPHY AND CLINICAL NEUROPHYSIOLOGY, 1991, 78 (06) :413-423

[2]

ALEMA G, 1959, Riv Sper Freniatr Med Leg Alien Ment, V83(4)Suppl, P1485

[3] GERSTMANN-STRAUSSLER SYNDROME - A VARIANT TYPE - AMYLOID PLAQUES AND ALZHEIMERS NEUROFIBRILLARY TANGLES IN CEREBRAL-CORTEX [J].

AMANO, N ;

YAGISHITA, S ;

YOKOI, S ;

ITOH, Y ;

KINOSHITA, J ;

MIZUTANI, T ;

MATSUISHI, T .

ACTA NEUROPATHOLOGICA, 1992, 84 (01) :15-23

[4] PRION PROTEIN IS ABNORMALLY ACCUMULATED IN INCLUSION-BODY MYOSITIS [J].

ASKANAS, V ;

BILAK, M ;

ENGEL, WK ;

ALVAREZ, RB ;

TOME, F ;

LECLERC, A .

NEUROREPORT, 1993, 5 (01) :25-28

[5]

BAKER HF, 1993, INT J EXP PATHOL, V74, P441

[6] CREUTZFELDT-JAKOB DISEASE WITH SEVERE INVOLVEMENT OF CEREBRAL WHITE MATTER AND CEREBELLUM [J].

BERCIANO, J ;

BERCIANO, MT ;

POLO, JM ;

FIGOLS, J ;

CIUDAD, J ;

LAFARGA, M .

VIRCHOWS ARCHIV A-PATHOLOGICAL ANATOMY AND HISTOPATHOLOGY, 1990, 417 (06) :533-538

[7] FAMILIAL CREUTZFELDT-JAKOB DISEASE (CODON-200 MUTATION) WITH SUPRANUCLEAR PALSY [J].

BERTONI, JM ;

BROWN, P ;

GOLDFARB, LG ;

RUBENSTEIN, R ;

GAJDUSEK, DC .

JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1992, 268 (17) :2413-2415

[8] Amyloid Precursor Protein (APP) and beta A4 Amyloid in the Etiology of Alzheimer's Disease: Precursor-Product Relationships in the Derangement of Neuronal Function [J].

Beyreuther, Konrad ;

Masters, Colin L. .

BRAIN PATHOLOGY, 1991, 1 (04) :241-251

[9]

BOLTON DC, 1982, SCIENCE, V23, P1309

[10]

BOUDIN G., 1965, REV NEUROL [PARTS], V113, P73

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