THE NOSOLOGY OF CREUTZFELDT-JAKOB-DISEASE AND CONDITIONS RELATED TO THE ACCUMULATION OF PRPCJD IN THE NERVOUS-SYSTEM

被引：68

作者：

RICHARDSON, EP

MASTERS, CL

机构：

[1] UNIV MELBOURNE,DEPT PATHOL,PARKVILLE,VIC 3052,AUSTRALIA

[2] MASSACHUSETTS GEN HOSP,CHARLES S KUBIK LAB NEUROPATHOL,BOSTON,MA 02114

来源：

BRAIN PATHOLOGY | 1995年 / 5卷 / 01期

关键词：

D O I：

10.1111/j.1750-3639.1995.tb00575.x

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

Although typical cases of Creutzfeldt-Jakob disease are readily recognized pathologically and clinically, variant forms often pose a diagnostic challenge. From the 1920's, when this disease was first characterized, until quite recently diagnosis relied heavily on morphologic changes. New advances in immunoassays and PrP gene analysis now provide important adjuncts in recognizing the spectrum of disorders of PrP metabolism associated with these transmissible encephalopathies.

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页码：33 / 41

页数：9

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