SUPERACTIVITY OF HUMAN PHOSPHORIBOSYL PYROPHOSPHATE SYNTHETASE DUE TO ALTERED REGULATION BY NUCLEOTIDE INHIBITORS AND INORGANIC-PHOSPHATE

被引:25
作者
BECKER, MA
LOSMAN, MJ
WILSON, J
SIMMONDS, HA
机构
[1] GUYS HOSP,PURINE LAB,LONDON SE1 9RT,ENGLAND
[2] HOSP SICK CHILDREN,DEPT NEUROL,LONDON WC1 35H,ENGLAND
关键词
D O I
10.1016/0304-4165(86)90151-0
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:168 / 176
页数:9
相关论文
共 36 条
  • [21] SELECTIVE EXPRESSION OF PHOSPHORIBOSYLPYROPHOSPHATE SYNTHETASE SUPERACTIVITY IN HUMAN LYMPHOBLAST LINES
    LOSMAN, MJ
    RIMON, D
    KIM, M
    BECKER, MA
    [J]. JOURNAL OF CLINICAL INVESTIGATION, 1985, 76 (04) : 1657 - 1664
  • [22] LOWRY OH, 1951, J BIOL CHEM, V193, P265
  • [23] MARTIN DW, 1972, J BIOL CHEM, V247, P5477
  • [24] ALTERED ISOELECTRIC PROPERTY OF A SUPERACTIVE 5-PHOSPHORIBOSYL-1-PYROPHOSPHATE (PRPP) SYNTHETASE IN A PATIENT WITH CLINICAL GOUT
    NISHIDA, Y
    AKAOKA, I
    HORIUCHI, Y
    [J]. BIOCHEMICAL MEDICINE, 1981, 26 (03): : 387 - 394
  • [25] A NEW DISORDER OF PURINE METABOLISM WITH BEHAVIORAL MANIFESTATIONS
    NYHAN, WL
    JAMES, JA
    TEBERG, AJ
    SWEETMAN, L
    NELSON, LG
    [J]. JOURNAL OF PEDIATRICS, 1969, 74 (01) : 20 - &
  • [26] ADENINE, HYPOXANTHINE AND GUANINE METABOLISM IN FIBROBLASTS FROM NORMAL INDIVIDUALS AND FROM PATIENTS WITH HYPOXANTHINE PHOSPHORIBOSYLTRANSFERASE DEFICIENCY
    RAIVIO, KO
    SEEGMILLER, JE
    [J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1973, 299 (02) : 273 - 282
  • [27] ROSENBLOOM FM, 1968, J BIOL CHEM, V243, P1166
  • [28] AN INBORN ERROR OF PURINE METABOLISM, DEAFNESS AND NEURODEVELOPMENTAL ABNORMALITY
    SIMMONDS, HA
    WEBSTER, DR
    LINGAM, S
    WILSON, J
    [J]. NEUROPEDIATRICS, 1985, 16 (02) : 106 - 108
  • [29] SIMMONDS HA, 1982, LANCET, V2, P68
  • [30] HUMAN ERYTHROCYTE PHOSPHORIBOSYLPYROPHOSPHATE SYNTHETASE MUTATIONALLY ALTERED IN REGULATORY PROPERTIES
    SPERLING, O
    PERSKYBR.S
    BOER, P
    DEVRIES, A
    [J]. BIOCHEMICAL MEDICINE, 1973, 7 (03): : 389 - 395