METHYLMALONIC SEMIALDEHYDE DEHYDROGENASE-DEFICIENCY - DEMONSTRATION OF DEFECTIVE VALINE AND BETA-ALANINE METABOLISM AND REDUCED MALONIC SEMIALDEHYDE DEHYDROGENASE-ACTIVITY IN CULTURED FIBROBLASTS

被引：16

作者：

GRAY, RGF

POLLITT, RJ

WEBLEY, J

机构：

[1] UNIV SHEFFIELD,DEPT PSYCHIAT,SHEFFIELD S10 2TN,S YORKSHIRE,ENGLAND

[2] UNIV SHEFFIELD,SUBDEPT MED GENET,SHEFFIELD S10 2TN,S YORKSHIRE,ENGLAND

来源：

BIOCHEMICAL MEDICINE AND METABOLIC BIOLOGY | 1987年 / 38卷 / 01期

关键词：

D O I：

10.1016/0885-4505(87)90069-7

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

收藏

页码：121 / 124

页数：4

相关论文

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