LABORATORY INVESTIGATION OF THE PORPHYRIAS

被引:82
作者
ELDER, GH
SMITH, SG
SMYTH, SJ
机构
[1] Department of Medical Biochemistry, University of Wales College of Medicine, Cardiff CF4 4XN, Wales, Heath Park
关键词
haem biosynthesis; porphobilinogen; porphyrias;
D O I
10.1177/000456329002700501
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
[No abstract available]
引用
收藏
页码:395 / 412
页数:18
相关论文
共 71 条
[61]   A PORPHYRIA CUTANEA TARDA-LIKE DISTRIBUTION PATTERN OF PORPHYRINS IN PLASMA, HEMODIALYSATE, HEMOFILTRATE, AND URINE OF PATIENTS ON CHRONIC-HEMODIALYSIS [J].
SEUBERT, S ;
SEUBERT, A ;
RUMPF, KW ;
KIFFE, H .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1985, 85 (02) :107-109
[62]  
Smith K., 1975, PORPHYRINS METALLOPO
[63]   USE OF THIN-LAYER CHROMATOGRAPHY IN SEPARATION OF FREE PORPHYRINS AND PORPHYRIN METHYL-ESTERS [J].
SMITH, SG .
BRITISH JOURNAL OF DERMATOLOGY, 1975, 93 (03) :291-295
[64]   PORPHYRIA-CUTANEA-TARDA, OR THE UROPORPHYRINOGEN DECARBOXYLASE DEFICIENCY DISEASES [J].
SWEENEY, GD .
CLINICAL BIOCHEMISTRY, 1986, 19 (01) :3-15
[65]   INHIBITION OF EHRLICHS REACTION OF PORPHOBILINOGEN BY INDICAN AND RELATED COMPOUNDS [J].
TADDEINI, L ;
KAY, IT ;
WATSON, CJ .
CLINICA CHIMICA ACTA, 1962, 7 (06) :890-&
[66]  
TISHLER PV, 1985, AM J PSYCHIAT, V142, P1430
[67]  
VALCARCEL M, 1987, CLIN CHEM, V33, P1826
[68]   GENETIC-ASPECTS OF ERYTHROPOIETIC PROTOPORPHYRIA [J].
WENT, LN ;
KLASEN, EC .
ANNALS OF HUMAN GENETICS, 1984, 48 (MAY) :105-117
[69]  
WESTERLUND J, 1988, CLIN CHEM, V34, P345
[70]   ION-EXCHANGE ANALYSIS OF PORPHYRINS IN URINE [J].
WITH, TK ;
PEDERSEN, JS .
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION, 1978, 38 (03) :279-284