EVIDENCE THAT MUTANT ENZYME IN FIBROBLASTS OF A PATIENT WITH MANNOSIDOSIS DOES NOT CROSSREACT WITH ANTISERUM RAISED AGAINST NORMAL ACIDIC ALPHA-D-MANNOSIDASE

被引:15
作者
BURDITT, LJ
CHOTAI, KA
WINCHESTER, BG
机构
关键词
D O I
10.1016/0014-5793(78)81168-5
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
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页码:186 / 189
页数:4
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共 17 条
  • [11] IMMUNOLOGICAL CROSS-REACTIVITY BETWEEN ALPHA-MANNOSIDASES FROM DIFFERENT SOURCES
    MERSMANN, G
    BUDDECKE, E
    [J]. INTERNATIONAL JOURNAL OF BIOCHEMISTRY, 1977, 8 (11): : 763 - 768
  • [12] MILLA PJ, 1977, ARCH DIS CHILDHOOD, V53, P937
  • [13] OCKERMAN PA, 1967, LANCET, V2, P239
  • [14] IMMUNOLOGICAL CHARACTERIZATION OF HUMAN LIVER ALPHA-D-MANNOSIDASE
    PHILLIPS, N
    ROBINSON, D
    WINCHESTER, B
    [J]. BIOCHEMICAL JOURNAL, 1975, 151 (03) : 469 - &
  • [15] CHARACTERIZATION OF HUMAN LIVER ALPHA-D-MANNOSIDASE PURIFIED BY AFFINITY CHROMATOGRAPHY
    PHILLIPS, NC
    ROBINSON, D
    WINCHESTER, BG
    [J]. BIOCHEMICAL JOURNAL, 1976, 153 (03) : 579 - 587
  • [16] PHILLIPS NC, 1977, BIOCH J, V163, P296
  • [17] MANNOSIDOSIS - DEFICIENCY OF A SPECIFIC ALPHA-MANNOSIDASE COMPONENT IN CULTURED FIBROBLASTS
    TAYLOR, HA
    THOMAS, GH
    AYLSWORTH, A
    STEVENSON, RE
    REYNOLDS, LW
    [J]. CLINICA CHIMICA ACTA, 1975, 59 (01) : 93 - 99