RECENTLY RECOGNIZED CONGENITAL MYASTHENIC SYNDROMES .A. ENDPLATE ACETYLCHOLINE (ACH) ESTERASE DEFICIENCY .B. PUTATIVE ABNORMALITY OF THE ACH INDUCED ION CHANNEL .C. PUTATIVE DEFECT OF ACH RESYNTHESIS OR MOBILIZATION - CLINICAL-FEATURES, ULTRASTRUCTURE AND CYTO-CHEMISTRY

被引：36

作者：

ENGEL, AG

LAMBERT, EH

MULDER, DM

GOMEZ, MR

WHITAKER, JN

HART, Z

SAHASHI, K

机构：

[1] UNIV TENNESSEE,CTR HLTH SCI,DEPT NEUROL,MEMPHIS,TN 38104

[2] CHILDRENS HOSP MICHIGAN,DEPT NEUROL,DETROIT,MI 48201

[3] AICHI MED SCH,NAGOYA,JAPAN

[4] MAYO CLIN & MAYO FDN,MUSCLE RES LAB,ROCHESTER,MN 55905

来源：

ANNALS OF THE NEW YORK ACADEMY OF SCIENCES | 1981年 / 377卷 / DEC期

关键词：

D O I：

10.1111/j.1749-6632.1981.tb33762.x

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：614 / 639

页数：26

共 44 条

[11]

Engel A G, 1979, Trans Am Neurol Assoc, V104, P8

[12] MORPHOMETRIC STUDY OF SKELETAL-MUSCLE ULTRASTRUCTURE [J].

ENGEL, AG ;

SANTA, T ;

STONNINGTON, HH ;

JERUSALEM, F ;

TSUJIHATA, M ;

BROWNELL, AKW ;

SAKAKIBARA, H ;

BANKER, BQ ;

SAHASHI, K ;

LAMBERT, EH .

MUSCLE & NERVE, 1979, 2 (03) :229-237

[13] STUDY OF LONG-TERM ANTICHOLINESTERASE THERAPY - EFFECTS ON NEUROMUSCULAR-TRANSMISSION AND ON MOTOR ENDPLATE FINE-STRUCTURE [J].

ENGEL, AG ;

LAMBERT, EH ;

SANTA, T .

NEUROLOGY, 1973, 23 (12) :1273-1281

[14] NEW MYASTHENIC SYNDROME WITH ENDPLATE ACETYLCHOLINESTERASE DEFICIENCY, SMALL NERVE-TERMINALS, AND REDUCED ACETYLCHOLINE-RELEASE [J].

ENGEL, AG ;

LAMBERT, EH ;

GOMEZ, MR .

ANNALS OF NEUROLOGY, 1977, 1 (04) :315-330

[15] ULTRASTRUCTURAL LOCALIZATION OF ACETYLCHOLINE-RECEPTOR IN MYASTHENIA-GRAVIS AND IN ITS EXPERIMENTAL AUTOIMMUNE MODEL [J].

ENGEL, AG ;

LINDSTROM, JM ;

LAMBERT, EH ;

LENNON, VA .

NEUROLOGY, 1977, 27 (04) :307-315

[16] MOTOR END PLATE IN MYASTHENIA-GRAVIS AND IN EXPERIMENTAL AUTOIMMUNE MYASTHENIA-GRAVIS - QUANTITATIVE ULTRASTRUCTURAL-STUDY [J].

ENGEL, AG ;

TSUJIHATA, M ;

LINDSTROM, JM ;

LENNON, VA .

ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1976, 274 (MAY28) :60-79

[17] ENTRY OF LABELED CALCIUM INTO INNERVATED REGION OF MOUSE DIAPHRAGM MUSCLE [J].

EVANS, RH .

JOURNAL OF PHYSIOLOGY-LONDON, 1974, 240 (03) :517-&

[18] NEUROMUSCULAR JUNCTION IN MYASTHENIA-GRAVIS - DECREASED ACETYLCHOLINE RECEPTORS [J].

FAMBROUGH, DM ;

DRACHMAN, DB ;

SATYAMURTI, S .

SCIENCE, 1973, 182 (4109) :293-295

[19] AN ANALYSIS OF THE END-PLATE POTENTIAL RECORDED WITH AN INTRA-CELLULAR ELECTRODE [J].

FATT, P ;

KATZ, B .

JOURNAL OF PHYSIOLOGY-LONDON, 1951, 115 (03) :320-370

[20] ACETYLCHOLINE-RECEPTOR DEGRADATION MEASURED BY DENSITY LABELING - EFFECTS OF CHOLINERGIC LIGANDS AND EVIDENCE AGAINST RECYCLING [J].

GARDNER, JM ;

FAMBROUGH, DM .

CELL, 1979, 16 (03) :661-674

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