PATHOGENESIS OF ALPHA-1-ANTITRYPSIN DEFICIENCY-ASSOCIATED LIVER-DISEASE, 1990

[31] TRANSPORT TO CELL-SURFACE OF INTESTINAL SUCRASE-ISOMALTASE IS BLOCKED IN THE GOLGI-APPARATUS IN A PATIENT WITH CONGENITAL SUCRASE-ISOMALTASE DEFICIENCY [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1985, 82 (13) : 4423 - 4427

[32] HEEB MJ, 1988, J BIOL CHEM, V263, P11613

[33] PREPARATION AND EXAMINATION OF THE OLIGOSACCHARIDES OF SERUM ALPHA-1-ANTITRYPSIN PIZ [J]. CANADIAN JOURNAL OF BIOCHEMISTRY AND CELL BIOLOGY, 1984, 62 (05): : 288 - 290

[34] HETEROZYGOUS MZ ALPHA-1-ANTITRYPSIN DEFICIENCY IN ADULTS WITH CHRONIC ACTIVE HEPATITIS AND CRYPTOGENIC CIRRHOSIS [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1981, 304 (10) : 557 - 560

[35] HOFKER M H, 1987, American Journal of Human Genetics, V41, pA220

[36] HUBBARD RC, 1988, AM J MED, V84, P52

[37] A SURPRISING NEW PROTEIN SUPERFAMILY CONTAINING OVALBUMIN, ANTI-THROMBIN-III, AND ALPHA1-PROTEINASE INHIBITOR [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1980, 95 (02) : 864 - 871

[38] AMINO-ACID SUBSTITUTION GLU-]LYS IN ALPHA-1-ANTITRYPSIN PIZ [J]. FEBS LETTERS, 1976, 65 (02) : 195 - 197

[39] HUMAN ALPHA-1-PROTEINASE INHIBITOR MECHANISM OF ACTION - EVIDENCE FOR ACTIVATION BY LIMITED PROTEOLYSIS [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1976, 72 (01) : 33 - 39

[40] SPECIES-SPECIFIC AND TISSUE-SPECIFIC EXPRESSION OF HUMAN ALPHA1-ANTITRYPSIN IN TRANSGENIC MICE [J]. GENES & DEVELOPMENT, 1987, 1 (02) : 161 - 171

[31] TRANSPORT TO CELL-SURFACE OF INTESTINAL SUCRASE-ISOMALTASE IS BLOCKED IN THE GOLGI-APPARATUS IN A PATIENT WITH CONGENITAL SUCRASE-ISOMALTASE DEFICIENCY [J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1985, 82 (13) : 4423 - 4427

[32] HEEB MJ, 1988, J BIOL CHEM, V263, P11613

[33] PREPARATION AND EXAMINATION OF THE OLIGOSACCHARIDES OF SERUM ALPHA-1-ANTITRYPSIN PIZ [J]. CANADIAN JOURNAL OF BIOCHEMISTRY AND CELL BIOLOGY, 1984, 62 (05): : 288 - 290

[34] HETEROZYGOUS MZ ALPHA-1-ANTITRYPSIN DEFICIENCY IN ADULTS WITH CHRONIC ACTIVE HEPATITIS AND CRYPTOGENIC CIRRHOSIS [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1981, 304 (10) : 557 - 560

[35] HOFKER M H, 1987, American Journal of Human Genetics, V41, pA220

[36] HUBBARD RC, 1988, AM J MED, V84, P52

[37] A SURPRISING NEW PROTEIN SUPERFAMILY CONTAINING OVALBUMIN, ANTI-THROMBIN-III, AND ALPHA1-PROTEINASE INHIBITOR [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1980, 95 (02) : 864 - 871

[38] AMINO-ACID SUBSTITUTION GLU-]LYS IN ALPHA-1-ANTITRYPSIN PIZ [J]. FEBS LETTERS, 1976, 65 (02) : 195 - 197

[39] HUMAN ALPHA-1-PROTEINASE INHIBITOR MECHANISM OF ACTION - EVIDENCE FOR ACTIVATION BY LIMITED PROTEOLYSIS [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1976, 72 (01) : 33 - 39

[40] SPECIES-SPECIFIC AND TISSUE-SPECIFIC EXPRESSION OF HUMAN ALPHA1-ANTITRYPSIN IN TRANSGENIC MICE [J]. GENES & DEVELOPMENT, 1987, 1 (02) : 161 - 171